About: Congenital hepatic fibrosis

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Congenital hepatic fibrosis is an inherited associated with proliferation of interlobular bile ducts within the portal areas and fibrosis that do not alter hepatic lobular architecture. The fibrosis would affect resistance in portal veins leading to portal hypertension.

Attributes	Values
rdf:type	Thing Disease yago:WikicatAutosomalRecessiveDisorders yago:Abstraction100002137 yago:Attribute100024264 yago:Condition113920835 yago:Disease114070360 yago:Disorder114052403 yago:IllHealth114052046 yago:Illness114061805 yago:PathologicalState114051917 yago:PhysicalCondition114034177 disease yago:State100024720 umbel-rc:AilmentCondition
rdfs:label	Congenital hepatic fibrosis (en) Kongenitale Leberfibrose (de)
rdfs:comment	Die kongenitale Leberfibrose (KLF), oft auch kongenitale hepatische Fibrose (CHF von englisch Congenital hepatic fibrosis) genannt, ist eine autosomal-rezessive Erbkrankheit, die zu einer Vernarbung der Lebergefäße führt. Sie ist meist mit anderen Syndromen, wie beispielsweise dem Meckel-Gruber-Syndrom, dem Jeune-Syndrom, dem Ivemark-Syndrom I, der autosomal-rezessiven polyzystischen Nierenerkrankung (ARPKD), der tuberösen Sklerose und vaginaler Atresie, assoziiert. (de) Congenital hepatic fibrosis is an inherited associated with proliferation of interlobular bile ducts within the portal areas and fibrosis that do not alter hepatic lobular architecture. The fibrosis would affect resistance in portal veins leading to portal hypertension. (en)
foaf:name	Congenital hepatic fibrosis (en)
name	Congenital hepatic fibrosis (en)
foaf:depiction
dct:subject	Autosomal recessive disorders Diseases of liver
Wikipage page ID	12022813 (xsd:integer)
Wikipage revision ID	1076900456 (xsd:integer)
Link from a Wikipage to another Wikipage	Caroli disease Cholangitis (disambiguation) Autosomal recessive disorders Diseases of liver Hepatocytes Hepatomegaly Heredity Polycystic kidney disease Portal hypertension Fibrosis Animal embryonic development Recessive gene Gestation Biliary hamartomas Cholangiocytes Gasteroenterology Von Meyenburg complex Hepatic lobule dbr:Duct_plate dbr:Fibrocystic_liver_disease
Link from a Wikipage to an external page	https://www.ncbi.nlm.nih.gov/bookshelf/br.fcgi%3Fbook=gene&part=hepatic-fibrosis
sameAs	Congenital hepatic fibrosis Congenital hepatic fibrosis Congenital hepatic fibrosis Congenital hepatic fibrosis Congenital hepatic fibrosis
dbp:wikiPageUsesTemplate	dbt:Cn dbt:Infobox_medical_condition_(new) dbt:Medical_resources dbt:Reflist dbt:Disease-stub dbt:Cystic_diseases
thumbnail	wiki-commons:Special:FilePath/autorecessive.svg?width=300
caption	Congenital hepatic fibrosis has an autosomal recessive pattern of inheritance. (en)
field	Gasteroenterology
has abstract	Die kongenitale Leberfibrose (KLF), oft auch kongenitale hepatische Fibrose (CHF von englisch Congenital hepatic fibrosis) genannt, ist eine autosomal-rezessive Erbkrankheit, die zu einer Vernarbung der Lebergefäße führt. Sie ist meist mit anderen Syndromen, wie beispielsweise dem Meckel-Gruber-Syndrom, dem Jeune-Syndrom, dem Ivemark-Syndrom I, der autosomal-rezessiven polyzystischen Nierenerkrankung (ARPKD), der tuberösen Sklerose und vaginaler Atresie, assoziiert. (de) Congenital hepatic fibrosis is an inherited associated with proliferation of interlobular bile ducts within the portal areas and fibrosis that do not alter hepatic lobular architecture. The fibrosis would affect resistance in portal veins leading to portal hypertension. (en)
eMedicineSubj	ped (en)
eMedicineTopic	459 (xsd:integer)
gold:hypernym	Disease
dbp:wordnet_type	http://www.w3.org/2006/03/wn/wn20/instances/synset-disease-noun-1
eMedicine subject	ped (en)
eMedicine topic	459 (en)
prov:wasDerivedFrom	wikipedia-en:Congenital_hepatic_fibrosis?oldid=1076900456&ns=0
page length (characters) of wiki page	3486 (xsd:nonNegativeInteger)
foaf:isPrimaryTopicOf	wikipedia-en:Congenital_hepatic_fibrosis
is Link from a Wikipage to another Wikipage of	Caroli disease List of diseases (C) Liver cancer Juvenile hemochromatosis COACH syndrome Portal hypertension Green ribbon Peliosis hepatis
is foaf:primaryTopic of	wikipedia-en:Congenital_hepatic_fibrosis

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