About: Post-transplant lymphoproliferative disorder     Goto   Sponge   NotDistinct   Permalink

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Post-transplant lymphoproliferative disorder (PTLD) is the name given to a B cell proliferation due to therapeutic immunosuppression after organ transplantation. These patients may develop infectious mononucleosis-like lesions or polyclonal polymorphic B-cell hyperplasia. Some of these B cells may undergo mutations which will render them malignant, giving rise to a lymphoma. In some patients, the malignant cell clone can become the dominant proliferating cell type, leading to frank lymphoma, a group of B cell lymphomas occurring in immunosuppressed patients following organ transplant.

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rdfs:label
  • Lymphoproliferative Erkrankung nach Transplantation (de)
  • Malattia linfoproliferativa post-trapianto (it)
  • Post-transplant lymphoproliferative disorder (en)
rdfs:comment
  • Als Lymphoproliferative Erkrankung nach Transplantation oder als Posttransplantations-Lymphoproliferative Erkrankung, nach der englischsprachigen Bezeichnung Post-Transplant Lymphoproliferative Disorder abgekürzt als PTLD, werden verschiedene lymphom-artige Erkrankungen bezeichnet, die nach einer Organtransplantation oder einer Stammzelltransplantation auftreten können. Es handelt sich dabei um eine Gruppe von histologisch und molekularbiologisch heterogenen Krankheiten, deren Spektrum von gutartigen Vermehrungen der T- und B-Lymphozyten bis zu malignen Lymphomen reicht. Die PTLD ist nach dem Kaposi-Sarkom und anderen Hautkrebserkrankungen die zweithäufigste tumorartige Erkrankung nach einer Organtransplantation. (de)
  • Post-transplant lymphoproliferative disorder (PTLD) is the name given to a B cell proliferation due to therapeutic immunosuppression after organ transplantation. These patients may develop infectious mononucleosis-like lesions or polyclonal polymorphic B-cell hyperplasia. Some of these B cells may undergo mutations which will render them malignant, giving rise to a lymphoma. In some patients, the malignant cell clone can become the dominant proliferating cell type, leading to frank lymphoma, a group of B cell lymphomas occurring in immunosuppressed patients following organ transplant. (en)
  • Con l'espressione malattia linfoproliferativa post-trapianto, nota anche con l'acronimo inglese PTLD (post-transplant lymphoproliferative disorder) si comprende un gruppo di malattie linfoproliferative, accomunate cioè dalla proliferazione patologica di linfociti, benigne e maligne, che possono manifestarsi nelle persone portatrici di trapianto d'organo in terapia immunosoppressiva. Si ritiene che nella patogenesi della malattia sia coinvolto il virus di Epstein-Barr. (it)
foaf:name
  • Post-transplant lymphoproliferative disorder (en)
name
  • Post-transplant lymphoproliferative disorder (en)
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DiseasesDB
ICD
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  • PTLD (en)
has abstract
  • Als Lymphoproliferative Erkrankung nach Transplantation oder als Posttransplantations-Lymphoproliferative Erkrankung, nach der englischsprachigen Bezeichnung Post-Transplant Lymphoproliferative Disorder abgekürzt als PTLD, werden verschiedene lymphom-artige Erkrankungen bezeichnet, die nach einer Organtransplantation oder einer Stammzelltransplantation auftreten können. Es handelt sich dabei um eine Gruppe von histologisch und molekularbiologisch heterogenen Krankheiten, deren Spektrum von gutartigen Vermehrungen der T- und B-Lymphozyten bis zu malignen Lymphomen reicht. Die PTLD ist nach dem Kaposi-Sarkom und anderen Hautkrebserkrankungen die zweithäufigste tumorartige Erkrankung nach einer Organtransplantation. (de)
  • Post-transplant lymphoproliferative disorder (PTLD) is the name given to a B cell proliferation due to therapeutic immunosuppression after organ transplantation. These patients may develop infectious mononucleosis-like lesions or polyclonal polymorphic B-cell hyperplasia. Some of these B cells may undergo mutations which will render them malignant, giving rise to a lymphoma. In some patients, the malignant cell clone can become the dominant proliferating cell type, leading to frank lymphoma, a group of B cell lymphomas occurring in immunosuppressed patients following organ transplant. (en)
  • Con l'espressione malattia linfoproliferativa post-trapianto, nota anche con l'acronimo inglese PTLD (post-transplant lymphoproliferative disorder) si comprende un gruppo di malattie linfoproliferative, accomunate cioè dalla proliferazione patologica di linfociti, benigne e maligne, che possono manifestarsi nelle persone portatrici di trapianto d'organo in terapia immunosoppressiva. Si ritiene che nella patogenesi della malattia sia coinvolto il virus di Epstein-Barr. (it)
eMedicineSubj
  • ped (en)
eMedicineTopic
ICDO
  • M9970/1 (en)
gold:hypernym
dbp:wordnet_type
ICD9
  • 238.77
eMedicine subject
  • ped (en)
eMedicine topic
  • 2851 (en)
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DiseasesDB
  • 34154
ICD10
  • D47.Z1
ICDO
  • M9970/1
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