. . "Aminoaciduria"@en . "Aminoaciduria \u2013 obecno\u015B\u0107 aminokwas\u00F3w w moczu. W warunkach prawid\u0142owych aminokwasy wyst\u0119puj\u0105 w moczu w niewielkiej ilo\u015Bci, natomiast zwi\u0119kszenie ich poziomu jest objawem patologicznym. Ca\u0142kowita ilo\u015B\u0107 aminokwas\u00F3w wydalanych w ci\u0105gu doby z moczem u ludzi zdrowych nie zale\u017Cy od stosowanej diety i wynosi 4\u20138 mmol. Dieta mo\u017Ce jednak wp\u0142ywa\u0107 na wydalanie poszczeg\u00F3lnych aminokwas\u00F3w i na przyk\u0142ad spo\u017Cywanie du\u017Cej ilo\u015Bci mi\u0119sa zwi\u0119ksza w moczu st\u0119\u017Cenie histydyny i . Zwi\u0119kszone st\u0119\u017Cenie aminokwas\u00F3w w moczu mo\u017Ce pojawia\u0107 si\u0119 fizjologicznie w ci\u0105\u017Cy. Patologiczne, zwi\u0119kszone wydalanie z moczem aminokwas\u00F3w mo\u017Ce wyst\u0119powa\u0107 w: \n* chorobach w\u0105troby \n* nadczynno\u015Bci tarczycy \n* nowotworach \n* oparzeniach \n* urazach \n* fenyloketonurii \n* chorobie Wilsona \n* galaktozemii \n* zatruciach (fosfor, rt\u0119\u0107, o\u0142\u00F3w, kwas szczawiowy, bizmut, kadm) \n* zespole nerczycowym \n* zespole Fanconiego \n* krzywicy \n* zaawansowanej niedokrwisto\u015Bci z niedoboru witaminy B12 \n* porfirii ostrej przerywanej"@pl . . . "Aminoazidurie"@de . "Aminoazidurie ist die Ausscheidung von Aminos\u00E4uren \u00FCber den Urin. Geringe Aminos\u00E4uremengen k\u00F6nnen auch bei Gesunden auftreten. Eine Pathologie liegt bei vermehrter Ausscheidung von Aminos\u00E4uren im Urin vor und wird mit Hyperaminoazidurie bezeichnet, allerdings werden beide Begriffe h\u00E4ufig synonym verwendet. Als vermehrt gilt, wenn mehr als 5 % der glomerul\u00E4r filtrierten Aminos\u00E4uren nicht r\u00FCckresorbiert, sondern ausgeschieden werden."@de . . . "Aminoaciduria occurs when the urine contains abnormally high amounts of amino acids. In the healthy kidney, the glomeruli filter all amino acids out of the blood, and the renal tubules then reabsorb over 95% of the filtered amino acids back into the blood."@en . . . . "Aminoaciduria es un t\u00E9rmino m\u00E9dico que designa la presencia anormal de amino\u00E1cidos en la orina. Es normal encontrar peque\u00F1as cantidades de amino\u00E1cidos en orina, sin embargo el incremento de los niveles considerados normales es un s\u00EDntoma que puede indicar la existencia de distintas enfermedades, por ejemplo la fenilcetonuria.\u200B"@es . . . "Urine amino acids"@en . . . . "3769"^^ . . . "Severe protein loss in the blood"@en . "Aminoaciduria es un t\u00E9rmino m\u00E9dico que designa la presencia anormal de amino\u00E1cidos en la orina. Es normal encontrar peque\u00F1as cantidades de amino\u00E1cidos en orina, sin embargo el incremento de los niveles considerados normales es un s\u00EDntoma que puede indicar la existencia de distintas enfermedades, por ejemplo la fenilcetonuria.\u200B"@es . . "4957376"^^ . "003366" . . "\u0628\u064A\u0644\u0629 \u062D\u0645\u0636\u0645\u064A\u0646\u064A\u0629"@ar . "14901"^^ . . . "Aminoaciduria \u2013 obecno\u015B\u0107 aminokwas\u00F3w w moczu. W warunkach prawid\u0142owych aminokwasy wyst\u0119puj\u0105 w moczu w niewielkiej ilo\u015Bci, natomiast zwi\u0119kszenie ich poziomu jest objawem patologicznym. Ca\u0142kowita ilo\u015B\u0107 aminokwas\u00F3w wydalanych w ci\u0105gu doby z moczem u ludzi zdrowych nie zale\u017Cy od stosowanej diety i wynosi 4\u20138 mmol. Dieta mo\u017Ce jednak wp\u0142ywa\u0107 na wydalanie poszczeg\u00F3lnych aminokwas\u00F3w i na przyk\u0142ad spo\u017Cywanie du\u017Cej ilo\u015Bci mi\u0119sa zwi\u0119ksza w moczu st\u0119\u017Cenie histydyny i . Zwi\u0119kszone st\u0119\u017Cenie aminokwas\u00F3w w moczu mo\u017Ce pojawia\u0107 si\u0119 fizjologicznie w ci\u0105\u017Cy."@pl . . . . . . "Aminoaciduria"@pl . "3366"^^ . "Aminoaciduria"@es . . "14901" . . "1100634192"^^ . . . . . . "Aminoaciduria"@en . "Severe protein loss in the blood" . "Aminoaciduria"@en . 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"35912001"^^ . . . . . . "Aminoazidurie ist die Ausscheidung von Aminos\u00E4uren \u00FCber den Urin. Geringe Aminos\u00E4uremengen k\u00F6nnen auch bei Gesunden auftreten. Eine Pathologie liegt bei vermehrter Ausscheidung von Aminos\u00E4uren im Urin vor und wird mit Hyperaminoazidurie bezeichnet, allerdings werden beide Begriffe h\u00E4ufig synonym verwendet. Als vermehrt gilt, wenn mehr als 5 % der glomerul\u00E4r filtrierten Aminos\u00E4uren nicht r\u00FCckresorbiert, sondern ausgeschieden werden."@de . . . . . . "Aminoaciduria occurs when the urine contains abnormally high amounts of amino acids. In the healthy kidney, the glomeruli filter all amino acids out of the blood, and the renal tubules then reabsorb over 95% of the filtered amino acids back into the blood. In overflow aminoaciduria, abnormally high concentrations of amino acids in the blood plasma overwhelm the resorptive capacity of the renal tubules, resulting in high concentrations of amino acids in the urine. This may be caused by congenital disorders of amino acid metabolism, for example, phenylketonuria, or may be secondary to liver disease. In renal aminoaciduria, the renal tubules are unable to reabsorb the filtered amino acids back into the blood, causing high concentrations of amino acids in the urine. This may be caused by a defect in the transport proteins in the renal tubule, for example, as occurs in Hartnup disease, or may be due to damage to the kidney tubule, for example, as occurs in Fanconi syndrome."@en . "Share of amino acid in various human diets and the resulting mix of amino acids in human blood serum. Glutamate and glutamine are the most frequent in food at over 10%, while alanine, glutamine, and glycine are the most common in blood."@en . . 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