"Diffuse myelinoclastic sclerosis, sometimes referred to as Schilder's disease, is a very infrequent neurodegenerative disease that presents clinically as pseudotumoural demyelinating lesions, making its diagnosis difficult. It usually begins in childhood, affecting children between 5 and 14 years old, but cases in adults are also possible."@en . "D002549"@en . . "Choroba Schildera (rozlane stwardnienie m\u00F3zgu, ang. diffuse myelinoclastic sclerosis) \u2013 rzadka choroba demielinizacyjna, zazwyczaj traktowana jako wariant stwardnienia rozsianego. Zazwyczaj choruj\u0105 dzieci mi\u0119dzy 5. a 14. rokiem \u017Cycia."@pl . . "272100"^^ . . "341.1" . . "G37.0" . "Diffuse myelinoclastic sclerosis"@en . . . . . "9220"^^ . . . "Esclerose difusa"@pt . . . "Choroba Schildera"@pl . . . . . "92"^^ . . . "Diffuse myelinoclastic sclerosis"@en . . . . "Choroba Schildera (rozlane stwardnienie m\u00F3zgu, ang. diffuse myelinoclastic sclerosis) \u2013 rzadka choroba demielinizacyjna, zazwyczaj traktowana jako wariant stwardnienia rozsianego. Zazwyczaj choruj\u0105 dzieci mi\u0119dzy 5. a 14. rokiem \u017Cycia."@pl . . . . "1046334725"^^ . "11849"^^ . . . . . . . . . "22994605"^^ . . "272100"^^ . "A esclerose difusa, por vezes referida como , \u00E9 uma doen\u00E7a neurodegenerativa rara que se manifesta trav\u00E9s de pseudotumores em les\u00F5es desmielinizantes, que tornam o diagn\u00F3stico dif\u00EDcil. Normalmente tem in\u00EDcio durante a inf\u00E2ncia, afectando sobretudo crian\u00E7as entre os 5 e os 14 anos de idade, embora tamb\u00E9m existam casos em adultos."@pt . "\u062A\u0635\u0644\u0628 \u0627\u0644\u0645\u0627\u064A\u0644\u064A\u0646 \u0627\u0644\u0645\u0646\u062A\u0634\u0631"@ar . "92"@en . "D002549" . . . . . . . "Diffuse myelinoclastic sclerosis"@en . . "neuro"@en . . . . "Diffuse myelinoclastic sclerosis, sometimes referred to as Schilder's disease, is a very infrequent neurodegenerative disease that presents clinically as pseudotumoural demyelinating lesions, making its diagnosis difficult. It usually begins in childhood, affecting children between 5 and 14 years old, but cases in adults are also possible. This disease is considered one of the borderline forms of multiple sclerosis because some authors consider them different diseases and others MS variants. Other diseases in this group are neuromyelitis optica (NMO), Balo concentric sclerosis and Marburg multiple sclerosis."@en . "11849" . "341.1"^^ . "neuro"@en . ""@en . "(Schilderova) difuzn\u00ED skler\u00F3za, zn\u00E1m\u00E1 t\u00E9\u017E jako Schilderova nemoc, je velmi vz\u00E1cn\u00E9 neurodegenerativn\u00ED onemocn\u011Bn\u00ED, kter\u00E9 se klinicky projevuje jako pseudotumorov\u00E1 demyeliniza\u010Dn\u00ED l\u00E9ze. Nemoc obvykle za\u010D\u00EDn\u00E1 v d\u011Btstv\u00ED a postihuje d\u011Bti ve v\u011Bku 5 a\u017E 14 let. Onemocn\u011Bn\u00ED dosp\u011Bl\u00FDch je v\u0161ak tak\u00E9 mo\u017En\u00E9. Nemoc je pova\u017Eov\u00E1na za jednu z hrani\u010Dn\u00EDch forem roztrou\u0161en\u00E9 skler\u00F3zy (RS). Symptomy jsou podobn\u00E9 jako u RS a mohou zahrnovat demenci, af\u00E1zii, , zm\u011Bny osobnosti, zhor\u0161enou pozornost, tremory, inkontinenci, svalovou slabost, \u0161patnou stabilitu, bolesti hlavy, zvracen\u00ED a zhor\u0161en\u00ED zraku a \u0159e\u010Di."@cs . . . . . "(Schilderova) difuzn\u00ED skler\u00F3za, zn\u00E1m\u00E1 t\u00E9\u017E jako Schilderova nemoc, je velmi vz\u00E1cn\u00E9 neurodegenerativn\u00ED onemocn\u011Bn\u00ED, kter\u00E9 se klinicky projevuje jako pseudotumorov\u00E1 demyeliniza\u010Dn\u00ED l\u00E9ze. Nemoc obvykle za\u010D\u00EDn\u00E1 v d\u011Btstv\u00ED a postihuje d\u011Bti ve v\u011Bku 5 a\u017E 14 let. Onemocn\u011Bn\u00ED dosp\u011Bl\u00FDch je v\u0161ak tak\u00E9 mo\u017En\u00E9. Nemoc je pova\u017Eov\u00E1na za jednu z hrani\u010Dn\u00EDch forem roztrou\u0161en\u00E9 skler\u00F3zy (RS). Symptomy jsou podobn\u00E9 jako u RS a mohou zahrnovat demenci, af\u00E1zii, , zm\u011Bny osobnosti, zhor\u0161enou pozornost, tremory, inkontinenci, svalovou slabost, \u0161patnou stabilitu, bolesti hlavy, zvracen\u00ED a zhor\u0161en\u00ED zraku a \u0159e\u010Di. Nemoc popsal v roce 1912 Paul Ferdinand Schilder."@cs . . "A esclerose difusa, por vezes referida como , \u00E9 uma doen\u00E7a neurodegenerativa rara que se manifesta trav\u00E9s de pseudotumores em les\u00F5es desmielinizantes, que tornam o diagn\u00F3stico dif\u00EDcil. Normalmente tem in\u00EDcio durante a inf\u00E2ncia, afectando sobretudo crian\u00E7as entre os 5 e os 14 anos de idade, embora tamb\u00E9m existam casos em adultos."@pt . . . . "G37.0"@en . . "Difuzn\u00ED skler\u00F3za"@cs . "Dms"@en . . "\u0645\u0631\u0636 \u062A\u0635\u0644\u0628 \u0627\u0644\u0645\u0627\u064A\u0644\u064A\u0646 \u0627\u0644\u0645\u0646\u062A\u0634\u0631 (Diffuse myelinoclastic sclerosis)\u060C \u064A\u0639\u0631\u0641 \u0623\u062D\u064A\u0627\u0646\u064B\u0627 \u0628\u0640\"\u062F\u0627\u0621 \u0634\u064A\u0644\u062F\u0631\"\u060C \u0648\u0647\u0648 \u0645\u0631\u0636 \u0639\u0635\u0628\u064A \u0646\u0627\u062F\u0631 \u064A\u0638\u0647\u0631 \u0637\u0628\u064A\u064B\u0627 \u0639\u0644\u0649 \u0647\u064A\u0626\u0629 \u0622\u0641\u0627\u062A \u0627\u0644\u062A\u0647\u0627\u0628 \u0627\u0644\u0646\u062E\u0627\u0639 \u0627\u0644\u0648\u0631\u0645\u064A \u0627\u0644\u0643\u0627\u0630\u0628 \u0623\u0648 \u0645\u0632\u064A\u0644 \u0627\u0644\u0645\u064A\u0627\u0644\u064A\u0646\u060C \u0627\u0644\u0623\u0645\u0631 \u0627\u0644\u0630\u064A \u064A\u062C\u0639\u0644 \u0645\u0646 \u0627\u0644\u0635\u0639\u0628 \u062A\u0634\u062E\u064A\u0635 \u0630\u0644\u0643 \u0627\u0644\u0645\u0631\u0636. \u0648\u064A\u0628\u062F\u0623 \u0641\u064A \u0627\u0644\u063A\u0627\u0644\u0628 \u0645\u0646\u0630 \u0627\u0644\u0637\u0641\u0648\u0644\u0629\u060C \u0645\u0624\u062B\u0631\u064B\u0627 \u0639\u0644\u0649 \u0627\u0644\u0623\u0637\u0641\u0627\u0644 \u0645\u0627 \u0628\u064A\u0646 5 \u0623\u0639\u0648\u0627\u0645 \u064814 \u0639\u0627\u0645\u064B\u0627\u060C \u0648\u0645\u0646 \u0627\u0644\u0648\u0627\u0631\u062F \u062C\u062F\u064B\u0627 \u0623\u0646 \u064A\u0635\u0627\u0628 \u0627\u0644\u0628\u0627\u0644\u063A\u0648\u0646 \u0628\u0627\u0644\u0645\u0631\u0636 \u0646\u0641\u0633\u0647."@ar . . "\u0645\u0631\u0636 \u062A\u0635\u0644\u0628 \u0627\u0644\u0645\u0627\u064A\u0644\u064A\u0646 \u0627\u0644\u0645\u0646\u062A\u0634\u0631 (Diffuse myelinoclastic sclerosis)\u060C \u064A\u0639\u0631\u0641 \u0623\u062D\u064A\u0627\u0646\u064B\u0627 \u0628\u0640\"\u062F\u0627\u0621 \u0634\u064A\u0644\u062F\u0631\"\u060C \u0648\u0647\u0648 \u0645\u0631\u0636 \u0639\u0635\u0628\u064A \u0646\u0627\u062F\u0631 \u064A\u0638\u0647\u0631 \u0637\u0628\u064A\u064B\u0627 \u0639\u0644\u0649 \u0647\u064A\u0626\u0629 \u0622\u0641\u0627\u062A \u0627\u0644\u062A\u0647\u0627\u0628 \u0627\u0644\u0646\u062E\u0627\u0639 \u0627\u0644\u0648\u0631\u0645\u064A \u0627\u0644\u0643\u0627\u0630\u0628 \u0623\u0648 \u0645\u0632\u064A\u0644 \u0627\u0644\u0645\u064A\u0627\u0644\u064A\u0646\u060C \u0627\u0644\u0623\u0645\u0631 \u0627\u0644\u0630\u064A \u064A\u062C\u0639\u0644 \u0645\u0646 \u0627\u0644\u0635\u0639\u0628 \u062A\u0634\u062E\u064A\u0635 \u0630\u0644\u0643 \u0627\u0644\u0645\u0631\u0636. \u0648\u064A\u0628\u062F\u0623 \u0641\u064A \u0627\u0644\u063A\u0627\u0644\u0628 \u0645\u0646\u0630 \u0627\u0644\u0637\u0641\u0648\u0644\u0629\u060C \u0645\u0624\u062B\u0631\u064B\u0627 \u0639\u0644\u0649 \u0627\u0644\u0623\u0637\u0641\u0627\u0644 \u0645\u0627 \u0628\u064A\u0646 5 \u0623\u0639\u0648\u0627\u0645 \u064814 \u0639\u0627\u0645\u064B\u0627\u060C \u0648\u0645\u0646 \u0627\u0644\u0648\u0627\u0631\u062F \u062C\u062F\u064B\u0627 \u0623\u0646 \u064A\u0635\u0627\u0628 \u0627\u0644\u0628\u0627\u0644\u063A\u0648\u0646 \u0628\u0627\u0644\u0645\u0631\u0636 \u0646\u0641\u0633\u0647. \u064A\u064F\u0639\u062F \u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 \u0648\u0627\u062D\u062F\u064B\u0627 \u0645\u0646 \u0623\u0634\u0643\u0627\u0644 \u0627\u0644\u062D\u062F\u0648\u062F \u0627\u0644\u0641\u0627\u0635\u0644\u0629 \u0627\u0644\u062A\u0627\u0628\u0639\u0629 \u0644\u0644\u062A\u0635\u0644\u0628 \u0627\u0644\u0639\u0635\u0628\u064A \u0627\u0644\u0645\u062A\u0639\u062F\u062F\u061B \u0641\u0642\u062F \u064A\u0639\u062A\u0628\u0631\u0647 \u0628\u0639\u0636 \u0627\u0644\u0628\u0627\u062D\u062B\u064A\u0646 \u0645\u0631\u0636\u064B\u0627 \u0645\u062E\u062A\u0644\u0641\u064B\u0627 \u0648\u064A\u0646\u0638\u0631 \u0625\u0644\u064A\u0647 \u0622\u062E\u0631\u0648\u0646 \u0628\u0627\u0639\u062A\u0628\u0627\u0631\u0647 \u0623\u062D\u062F \u0623\u0646\u0648\u0627\u0639 \u0645\u0631\u0636 \u0627\u0644\u062A\u0635\u0644\u0628 \u0627\u0644\u0639\u0635\u0628\u064A \u0627\u0644\u0645\u062A\u0639\u062F\u062F. \u0648\u0645\u0646 \u0628\u064A\u0646 \u062A\u0644\u0643 \u0627\u0644\u0623\u0645\u0631\u0627\u0636 \u0641\u064A \u0646\u0641\u0633 \u0627\u0644\u0645\u062C\u0645\u0648\u0639\u0629 \u0647\u064A \u0627\u0644\u062A\u0647\u0627\u0628 \u0627\u0644\u0646\u062E\u0627\u0639 \u0648\u0627\u0644\u0623\u0639\u0635\u0627\u0628 \u0627\u0644\u0628\u0635\u0631\u064A (NMO)\u060C \u0648\u062A\u0635\u0644\u0628 \u0628\u0627\u0644\u0648 \u0645\u062A\u0645\u0631\u0643\u0632 (Balo concentric sclerosis)\u060C \u0648\u062A\u0635\u0644\u0628 \u0645\u0627\u0631\u0628\u0648\u0631\u063A \u0627\u0644\u0645\u062A\u0639\u062F\u062F (Marburg multiple sclerosis)."@ar . . .