. . . . "La granulomatosis con poliangitis (previamente conocida como Granulomatosis de Wegener) es un tipo de vasculitis poco frecuente en la cual se produce hinchaz\u00F3n e inflamaci\u00F3n de los vasos sangu\u00EDneos, dificultando as\u00ED el flujo de la sangre. Afecta principalmente los vasos sangu\u00EDneos en la nariz, senos paranasales, o\u00EDdos, pulmones y ri\u00F1ones, aunque otras \u00E1reas pueden estar comprometidas."@es . . . . . "D014890" . . "\u0397 \u03BA\u03BF\u03BA\u03BA\u03B9\u03C9\u03BC\u03B1\u03C4\u03CE\u03B4\u03B7\u03C2 \u03B1\u03B3\u03B3\u03B5\u03B9\u03AF\u03C4\u03B9\u03B4\u03B1 \u0392\u03AD\u03B3\u03BA\u03B5\u03BD\u03B5\u03C1 \u03B5\u03AF\u03BD\u03B1\u03B9 \u03BC\u03AF\u03B1 \u03C3\u03C0\u03AC\u03BD\u03B9\u03B1\u03C2 \u03C3\u03C5\u03C3\u03C4\u03B7\u03BC\u03B1\u03C4\u03B9\u03BA\u03AE \u03B1\u03B3\u03B3\u03B5\u03B9\u03AF\u03C4\u03B9\u03B4\u03B1 \u03C4\u03C9\u03BD \u03BC\u03B9\u03BA\u03C1\u03BF\u03CD \u03BC\u03B5\u03B3\u03AD\u03B8\u03BF\u03C5\u03C2 \u03B1\u03B3\u03B3\u03B5\u03AF\u03C9\u03BD \u03C4\u03BF\u03C5 \u03B1\u03AF\u03BC\u03B1\u03C4\u03BF\u03C2 \u03C0.\u03C7. \u03C6\u03BB\u03B5\u03B2\u03AF\u03B4\u03B9\u03B1, \u03B1\u03C1\u03C4\u03B7\u03C1\u03AF\u03B4\u03B9\u03B1 \u03BA\u03B1\u03B9 \u03C4\u03C1\u03B9\u03C7\u03BF\u03B5\u03B9\u03B4\u03AE. \u03A0\u03C1\u03BF\u03C3\u03B2\u03AC\u03BB\u03BB\u03B5\u03B9 \u03C4\u03BF \u03B1\u03BD\u03CE\u03C4\u03B5\u03C1\u03BF \u03B1\u03BD\u03B1\u03C0\u03BD\u03B5\u03C5\u03C3\u03C4\u03B9\u03BA\u03CC \u03C3\u03CD\u03C3\u03C4\u03B7\u03BC\u03B1 (\u03BC\u03CD\u03C4\u03B7, \u03C3\u03C4\u03CC\u03BC\u03B1, \u03C6\u03AC\u03C1\u03C5\u03B3\u03B3\u03B1, \u03BB\u03AC\u03C1\u03C5\u03B3\u03B3\u03B1, \u03C4\u03C1\u03B1\u03C7\u03B5\u03AF\u03B1, \u03B2\u03C1\u03CC\u03B3\u03C7\u03BF\u03B9), \u03C4\u03BF \u03BA\u03B1\u03C4\u03CE\u03C4\u03B5\u03C1\u03BF \u03B1\u03BD\u03B1\u03C0\u03BD\u03B5\u03C5\u03C3\u03C4\u03B9\u03BA\u03CC (\u03C0\u03BD\u03B5\u03CD\u03BC\u03BF\u03BD\u03B5\u03C2, \u03BD\u03B5\u03C6\u03C1\u03BF\u03CD\u03C2) \u03BA\u03B1\u03B8\u03CE\u03C2 \u03B5\u03C0\u03AF\u03C3\u03B7\u03C2 \u03BA\u03B1\u03B9 \u03AC\u03BB\u03BB\u03B1 \u03CC\u03C1\u03B3\u03B1\u03BD\u03B1. \u0394\u03B9\u03B1\u03BA\u03C1\u03AF\u03BD\u03B5\u03C4\u03B1\u03B9 \u03C3\u03B5 \u03B4\u03CD\u03BF \u03C4\u03CD\u03C0\u03BF\u03C5\u03C2 \u03B1\u03BD\u03AC\u03BB\u03BF\u03B3\u03B1 \u03BC\u03B5 \u03C4\u03B7\u03BD \u03C0\u03C1\u03BF\u03C3\u03B2\u03BF\u03BB\u03AE \u03BA\u03B1\u03B9 \u03C4\u03B7\u03BD \u03B5\u03BE\u03AC\u03C0\u03BB\u03C9\u03C3\u03AE \u03C4\u03BF\u03C5\u03C2 \u03C3\u03C4\u03BF\u03BD \u03BF\u03C1\u03B3\u03B1\u03BD\u03B9\u03C3\u03BC\u03CC."@el . "\u0413\u0440\u0430\u043D\u0443\u043B\u0451\u043C\u0430\u0442\u043E\u0437 \u0412\u0435\u0433\u0435\u043D\u0435\u0440\u0430"@ru . . . . . . ""@en . . . . . . . "\u591A\u767A\u8840\u7BA1\u708E\u6027\u8089\u82BD\u816B\u75C7\uFF08\u305F\u306F\u3064\u3051\u3063\u304B\u3093\u3048\u3093\u305B\u3044\u306B\u304F\u3052\u3057\u3085\u3057\u3087\u3046\u3001\u82F1\u8A9E: Granulomatosis with polyangiitis; GPA\uFF09\u306F1939\u5E74\u30C9\u30A4\u30C4\u306E\u75C5\u7406\u5B66\u8005Wegener\u306B\u3088\u308A\u5831\u544A\u3055\u308C\u305F\u3002\u304B\u3064\u3066\u306F\u3001\u30A6\u30A7\u30B2\u30CA\u30FC\u8089\u82BD\u816B\u75C7 (\u30A6\u30A7\u30B2\u30CA\u30FC\u306B\u304F\u3052\u3057\u3085\u3057\u3087\u3046\u3001\u82F1\u8A9E: Wegener's granulomatosis) \u3068\u306E\u540D\u79F0\u304C\u983B\u7528\u3055\u308C\u3066\u3044\u305F\u304C\u3001\u8840\u7BA1\u708E\u306E\u5206\u985E\u3092\u5B9A\u3081\u305FCHCC\u5206\u985E\u304C2012\u5E74\u306B\u6539\u8A02\u3055\u308C\u3001DHCC\u5206\u985E\u540D\u79F0\u306F\u300C\u591A\u767A\u8840\u7BA1\u708E\u6027\u8089\u82BD\u816B\u75C7 (Granulomatosis with polyangiitis)\u300D\u3068\u306A\u3063\u3066\u3044\u308B\u3002 \u5168\u8EAB\u6027\u306E\u8840\u7BA1\u708E\u3067\u3001\u4E2D - \u5C0F\u578B\u52D5\u8108\u3092\u50B7\u5BB3\u3059\u308B\u75BE\u60A3\u3002 \u9F3B\u3084\u306E\u3069\u306E\u50B7\u5BB3\u304B\u3089\u306F\u3058\u307E\u308B\u306E\u3067\u6700\u521D\u306F\u98A8\u90AA\u306E\u3088\u3046\u3067\u3082\u3042\u308B\u304C\u3001\u6025\u901F\u306B\u9593\u8CEA\u6027\u80BA\u708E\u3001\u6025\u901F\u9032\u884C\u6027\u7CF8\u7403\u4F53\u814E\u708E\u3092\u304D\u305F\u3059\u3002\u3057\u305F\u304C\u3063\u3066\u75C7\u72B6\u306F\u3001\u54B3\u3001\u547C\u5438\u56F0\u96E3\u3001\u6D6E\u816B\u306A\u3069\u3067\u3042\u308B\u3002\u8EFD\u5EA6\u306E\u767A\u71B1\u3082\u304A\u3053\u308B\u3002\u9F3B\u306B\u95A2\u3057\u3066\u3082\u5185\u90E8\u69CB\u9020\u304C\u7834\u58CA\u3055\u308C\u3001\u3064\u3076\u308C\u3066\u3092\u5448\u3059\u308B\u3053\u3068\u304C\u3042\u308B\u3002\u3001\u3076\u3069\u3046\u819C\u708E\u3001\u89D2\u819C\u6F70\u760D\u306A\u3069\u773C\u79D1\u7684\u75BE\u60A3\u3082\u8D77\u3053\u308B\u3053\u3068\u304C\u3042\u308B\u3002\u305D\u306E\u307B\u304B\u76AE\u819A\uFF08\u6709\u75DB\u6027\u7D05\u6591\uFF09\u3001\u795E\u7D4C\u3001\u8133\u3092\u304A\u304B\u3057\u3046\u308B\u3002 \u8840\u6DB2\u691C\u67FB\u3067\u306Fc-ANCA\uFF08PR3-ANCA\uFF09\u304C\u7279\u7570\u7684\u306B\u4E0A\u6607\u3059\u308B\u3002\u30B9\u30C6\u30ED\u30A4\u30C9\u5264\u306A\u3069\u306E\u6CBB\u7642\u3092\u3082\u3063\u3066\u3057\u3066\u3082\u304D\u308F\u3081\u3066\u91CD\u7BE4\u306A\u75BE\u60A3\u3067\u3042\u308B\u3002"@ja . . . . . . "\u8089\u82BD\u816B\u4F75\u591A\u767C\u6027\u8840\u7BA1\u708E\uFF08Granulomatosis with polyangiitis\uFF0C\u7E2E\u5BEBGPA\uFF09\uFF0C\u820A\u7A31\u97CB\u683C\u7D0D\u8089\u82BD\u816B\uFF08\u82F1\u8A9E\uFF1AWegener's granulomatosis\uFF0C\u7E2E\u5BEB\u70BA WG\uFF09\uFF0C\u53C8\u8B6F\u4F5C\u83EF\u683C\u7D0D\u6C0F\u8089\u82BD\u816B\uFF0C\u662F\u4E00\u7A2E\u81EA\u9AD4\u514D\u75AB\u75BE\u75C5\uFF0C\u767C\u751F\u539F\u56E0\u4E0D\u660E\uFF0C\u7279\u5FB5\u70BA\u60E1\u6027\u7684\u8840\u7BA1\u708E\uFF0C\u4E3B\u8981\u4FB5\u72AF\u4E0A\u3001\u4E0B\u547C\u5438\u9053\u53CA\u814E\u81DF\uFF0C\u6703\u5F71\u97FF\u9F3B\u5B50\u3001\u80BA\u3001\u814E\u81DF\u4EE5\u53CA\u5176\u4ED6\u5668\u5B98\u3002"@zh . . . . . . . . . "\u0413\u0440\u0430\u043D\u0443\u043B\u0435\u043C\u0430\u0442\u043E\u0301\u0437 \u0412\u0435\u0301\u0433\u0435\u043D\u0435\u0440\u0430 (\u0438\u0437\u0432\u0435\u0441\u0442\u0435\u043D \u0442\u0430\u043A\u0436\u0435 \u043A\u0430\u043A \u0433\u0440\u0430\u043D\u0443\u043B\u0435\u043C\u0430\u0442\u043E\u0301\u0437 \u0441 \u043F\u043E\u043B\u0438\u0430\u043D\u0433\u0438\u0438\u0301\u0442\u043E\u043C) \u2014 \u0430\u0443\u0442\u043E\u0438\u043C\u043C\u0443\u043D\u043D\u043E\u0435 \u0433\u0440\u0430\u043D\u0443\u043B\u0451\u043C\u0430\u0442\u043E\u0437\u043D\u043E\u0435 \u0432\u043E\u0441\u043F\u0430\u043B\u0435\u043D\u0438\u0435 \u0441\u0442\u0435\u043D\u043E\u043A \u0441\u043E\u0441\u0443\u0434\u043E\u0432 (\u0432\u0430\u0441\u043A\u0443\u043B\u0438\u0442), \u0437\u0430\u0445\u0432\u0430\u0442\u044B\u0432\u0430\u044E\u0449\u0435\u0435 \u043C\u0435\u043B\u043A\u0438\u0435 \u0438 \u0441\u0440\u0435\u0434\u043D\u0438\u0435 \u043A\u0440\u043E\u0432\u0435\u043D\u043E\u0441\u043D\u044B\u0435 \u0441\u043E\u0441\u0443\u0434\u044B: \u043A\u0430\u043F\u0438\u043B\u043B\u044F\u0440\u044B, \u0432\u0435\u043D\u0443\u043B\u044B, \u0430\u0440\u0442\u0435\u0440\u0438\u043E\u043B\u044B \u0438 \u0430\u0440\u0442\u0435\u0440\u0438\u0438, \u0441 \u0432\u043E\u0432\u043B\u0435\u0447\u0435\u043D\u0438\u0435\u043C \u0432\u0435\u0440\u0445\u043D\u0438\u0445 \u0434\u044B\u0445\u0430\u0442\u0435\u043B\u044C\u043D\u044B\u0445 \u043F\u0443\u0442\u0435\u0439, \u0433\u043B\u0430\u0437, \u043F\u043E\u0447\u0435\u043A, \u043B\u0451\u0433\u043A\u0438\u0445 \u0438 \u0434\u0440\u0443\u0433\u0438\u0445 \u043E\u0440\u0433\u0430\u043D\u043E\u0432. \u041E\u0442\u043D\u043E\u0441\u0438\u0442\u0441\u044F \u043A \u0441\u0438\u0441\u0442\u0435\u043C\u043D\u044B\u043C \u0410\u041D\u0426\u0410-\u0430\u0441\u0441\u043E\u0446\u0438\u0438\u0440\u043E\u0432\u0430\u043D\u043D\u044B\u043C \u043D\u0435\u043A\u0440\u043E\u0442\u0438\u0437\u0438\u0440\u0443\u044E\u0449\u0438\u043C \u0432\u0430\u0441\u043A\u0443\u043B\u0438\u0442\u0430\u043C."@ru . "Granulomatose com poliangiite, anteriormente denominada Granulomatose de Wegener ou doen\u00E7a de Wegener, \u00E9 uma rara doen\u00E7a autoimune, ou seja, uma doen\u00E7a que ataca elementos constitutivos normais do corpo humano, fazendo com que nossos anticorpos ataquem a n\u00F3s mesmos. \u00C9 importante ressaltar que a denomina\u00E7\u00E3o anterior de granulomatose de Wegener prestigiava Friederich Wegener, m\u00E9dico alem\u00E3o ardoroso filiado ao partido nazista, grande admirador de Hitler e com amplo conhecimento das atrocidades contra judeus e outras minorias. A Granulomatose com poliangiite \u00E9 uma forma de vasculite, que \u00E9 uma inflama\u00E7\u00E3o dos vasos sangu\u00EDneos, provocada pelo pr\u00F3prio sistema imunol\u00F3gico, afetando principalmente rins e pulm\u00F5es, apesar de eventualmente atingir outros \u00F3rg\u00E3os."@pt . . . . "2401"@en . . . . . . . . . . . . . . "Granulomat\u00F6s polyangit - (GPA) (tidigare Wegeners granulomatos) \u00E4r en ovanlig systemsjukdom som angriper finare blodk\u00E4rl (vaskulit) men som kan drabba alla k\u00E4rl, framf\u00F6r allt h\u00E4ndernas, f\u00F6tternas, luftv\u00E4garnas, n\u00E4sans och njurarnas k\u00E4rl. Upphostningar med blod, samt n\u00E4sblod \u00E4r vanligt. \u00D6gonen \u00E4r ofta drabbade. Det \u00E4r ocks\u00E5 vanligt att njurarna drabbas och om behandling inte s\u00E4tts in snabbt kan deras funktion kraftigt minska eller helt sl\u00E5s ut. Sjukdomen angriper dock inte endast dessa organ, utan hela kroppens blodomlopp kan drabbas och det \u00E4r s\u00E4rskilt de finare blodk\u00E4rlen (kapill\u00E4rerna) som angrips. Sjukdomen kan leda till subglottal stenos och granulombildningar i trachea eller under det subglottala rummet. Detta kan numera effektivt behandlas med laserkirurgi. I s\u00E4llsynta fall har man n"@sv . "Granulomatosis Wegener atau dikenal juga dengan granulomatosis dengan poliangitiis (GPA) adalah gangguan sistemik yang melibatkan dan . Kondisi ini terlihat dari inflamasi pembuluh darah yang melibatkan pembuluh kecil dan sedang di berbagai organ penting. Inflamasi di daerah paru dan ginjal bisa berakibat fatal. Penanganannya bisa dilakukan dengan melakukan supresi imunitas. \n* l \n* \n* s"@in . "Ziarniniakowato\u015B\u0107 z zapaleniem naczy\u0144 (dawniej: ziarniniak Wegenera, ziarniniakowato\u015B\u0107 Wegenera) \u2013 choroba uk\u0142adowa z martwiczym zapaleniem ma\u0142ych i \u015Brednich naczy\u0144, kt\u00F3ra obejmuje g\u0142\u00F3wnie g\u00F3rne drogi oddechowe, p\u0142uca i nerki."@pl . . . . "La granulomatosis con poliangitis (previamente conocida como Granulomatosis de Wegener) es un tipo de vasculitis poco frecuente en la cual se produce hinchaz\u00F3n e inflamaci\u00F3n de los vasos sangu\u00EDneos, dificultando as\u00ED el flujo de la sangre. Afecta principalmente los vasos sangu\u00EDneos en la nariz, senos paranasales, o\u00EDdos, pulmones y ri\u00F1ones, aunque otras \u00E1reas pueden estar comprometidas."@es . . . . "14057"^^ . . . "Granulomatosis with polyangiitis (GPA), previously known as Wegener's granulomatosis (WG), is a rare long-term systemic disorder that involves the formation of granulomas and inflammation of blood vessels (vasculitis). It is a form of vasculitis that affects small- and medium-size vessels in many organs but most commonly affects the upper respiratory tract, lungs and kidneys. The signs and symptoms of GPA are highly varied and reflect which organs are supplied by the affected blood vessels. Typical signs and symptoms include nosebleeds, stuffy nose and crustiness of nasal secretions, and inflammation of the uveal layer of the eye. Damage to the heart, lungs and kidneys can be fatal."@en . . "28722"^^ . . "Granulomatosis with polyangiitis"@en . . "\u8089\u82BD\u816B\u4F75\u591A\u767C\u6027\u8840\u7BA1\u708E"@zh . "1121854168"^^ . . "794996"^^ . . . "446.4"^^ . . "Ziarniniakowato\u015B\u0107 z zapaleniem naczy\u0144 (dawniej: ziarniniak Wegenera, ziarniniakowato\u015B\u0107 Wegenera) \u2013 choroba uk\u0142adowa z martwiczym zapaleniem ma\u0142ych i \u015Brednich naczy\u0144, kt\u00F3ra obejmuje g\u0142\u00F3wnie g\u00F3rne drogi oddechowe, p\u0142uca i nerki."@pl . "Granulomatose met polyangiitis (GPA), ook bekend als de ziekte van Wegener of granulomatose van Wegener, is een vorm van systeemvasculitis, een auto-immuunziekte. GPA wordt gekenmerkt door ontstekingen van de wanden van de kleine bloedvaten. Deze ontstekingen kunnen zich in meerdere organen manifesteren. De bloedvatontstekingen leiden tot versterf (necrose) van weefsels in organen. Tevens treden vrij karakteristieke ophopingen van ontstekingscellen (granulomen) op, met name in de neus en de longen, maar ook de nieren worden vaak aangetast, evenals de huid, ogen, gewrichten, centraal en perifeer zenuwstelsel en maag- en darmkanaal. De ziekte kan in elk van de genoemde organen beginnen, zonder dat andere organen meedoen. Daardoor wordt de ziekte vooral in het begin niet herkend."@nl . . . . . . . . . . . "Granulomatosis with polyangiitis"@en . . "Granulomatosi associata a poliangioite"@it . . . . . . . "Ziarniniakowato\u015B\u0107 z zapaleniem naczy\u0144"@pl . "Die Granulomatose mit Polyangiitis (GPA) (fr\u00FCher Wegener-Granulomatose oder Morbus Wegener, benannt nach dem deutschen Pathologen Friedrich Wegener, Wegener-Klinger-Granulomatose, nach dem deutschen Pathologen Heinz Klinger) ist eine rheumatische Systemerkrankung des Gef\u00E4\u00DFsystems und gekennzeichnet durch eine nekrotisierende Entz\u00FCndung der Gef\u00E4\u00DFe (Vaskulitis) im Bereich des Kopfes, der Lunge und der Nieren, welche mit einer ulzerierenden Granulombildung der kleinen und mittleren Gef\u00E4\u00DFe in den oberen (Nase, Nasennebenh\u00F6hlen, Mittelohr, Oropharynx) und den unteren Atemwegen (Lunge) einhergeht. In 80 Prozent der F\u00E4lle kommt es zu einer Nierenk\u00F6rperchenentz\u00FCndung (Glomerulonephritis, genauer: Pauci-Immun-Glomerulonephritis als pathohistologisches Korrelat) und zur Bildung von Mikroaneurysmen in der Niere. Durch die Entz\u00FCndung der Gef\u00E4\u00DFe kommt es zu einer mangelhaften Blutversorgung der betroffenen Organe. Grunds\u00E4tzlich kann jegliches Gewebe betroffen sein."@de . . "Granulomatose met polyangiitis"@nl . . . "La granulomatosi associata a poliangioite (GPA dall'inglese Granulomatosis with polyangiitis) o granulomatosi di Wegener (dal nome di Friedrich Wegener, medico dell'esercito nazista), o poliangioite granulomatosa, \u00E8 una vasculite necrotizzante su base autoimmune dei piccoli e medi vasi che interessa il sistema respiratorio e frequentemente i reni. Insieme alla poliangioite microscopica e alla sindrome di Churg-Strauss, rientra nel gruppo delle vasculiti ANCA-associate, cio\u00E8 di quelle vasculiti caratterizzate dalla presenza in circolo degli anticorpi anti-citoplasma dei neutrofili (ANCA)."@it . . . . "\u591A\u767A\u8840\u7BA1\u708E\u6027\u8089\u82BD\u816B\u75C7"@ja . . "\u0648\u0631\u0627\u0645 \u062D\u0628\u064A\u0628\u064A \u0648\u064A\u063A\u0646\u0631\u064A"@ar . . . . . "M31.3"@en . "\u0391\u03B3\u03B3\u03B5\u03B9\u03AF\u03C4\u03B9\u03B4\u03B1 \u0392\u03AD\u03B3\u03BA\u03B5\u03BD\u03B5\u03C1"@el . . . . . "La granulomatosi associata a poliangioite (GPA dall'inglese Granulomatosis with polyangiitis) o granulomatosi di Wegener (dal nome di Friedrich Wegener, medico dell'esercito nazista), o poliangioite granulomatosa, \u00E8 una vasculite necrotizzante su base autoimmune dei piccoli e medi vasi che interessa il sistema respiratorio e frequentemente i reni. Insieme alla poliangioite microscopica e alla sindrome di Churg-Strauss, rientra nel gruppo delle vasculiti ANCA-associate, cio\u00E8 di quelle vasculiti caratterizzate dalla presenza in circolo degli anticorpi anti-citoplasma dei neutrofili (ANCA)."@it . . "\uB2E4\uBC1C\uD608\uAD00\uC5FC \uB3D9\uBC18 \uC721\uC544\uC885\uC99D(granulomatosis with polyangiitis; GPA) \uB610\uB294 \uBCA0\uAC8C\uB108 \uC721\uC544\uC885\uC99D(Wegener's granulomatosis; WG)\uC740 \uACFC \uC721\uC544\uC885\uC774 \uB3D9\uC2DC\uC5D0 \uB098\uD0C0\uB098\uB294 \uC870\uC9C1\uC7A5\uC560\uC774\uB2E4. \uD5C8\uD30C\uC640 \uC2E0\uC7A5\uC5D0 \uC190\uC0C1\uC744 \uC785\uD788\uBA70, \uC774 \uC190\uC0C1\uC740 \uB9E4\uC6B0 \uCE58\uBA85\uC801\uC774\uC5B4\uC11C \uC0DD\uBA85\uC744 \uC704\uD611\uD560 \uC218 \uC788\uB2E4. \uB9CC\uC131\uC801\uC778 \uBA74\uC5ED\uC5B5\uC81C\uB85C \uBC1C\uC0DD\uD560 \uC218 \uC788\uB2E4. \"\uBCA0\uAC8C\uB108 \uC721\uC544\uC885\"\uC774\uB780 \uBA85\uCE6D\uC740 1936\uB144 \uBCD1\uC744 \uBC1C\uACAC\uD55C \uC758 \uC774\uB984\uC774 \uBD99\uC740 \uAC83\uC774\uB2E4. 2000\uB144 \uBCA0\uAC8C\uB108\uAC00 \uB098\uCE58 \uB2F9\uC6D0\uC774\uC5C8\uC74C\uC774 \uBC1D\uD600\uC9C0\uC790 \uBCA0\uAC8C\uB108\uC758 \uC774\uB984\uC744 \uC5B8\uAE09\uD558\uB294 \uAC83\uC774 \uD130\uBD80\uC2DC\uB418\uC5B4 \uD604\uC7AC\uC758 \uC774\uB984\uC774 \uC0C8\uB85C \uBD99\uC5C8\uB2E4."@ko . . . . . . . . "Granulomat\u00F6s polyangit - (GPA) (tidigare Wegeners granulomatos) \u00E4r en ovanlig systemsjukdom som angriper finare blodk\u00E4rl (vaskulit) men som kan drabba alla k\u00E4rl, framf\u00F6r allt h\u00E4ndernas, f\u00F6tternas, luftv\u00E4garnas, n\u00E4sans och njurarnas k\u00E4rl. Upphostningar med blod, samt n\u00E4sblod \u00E4r vanligt. \u00D6gonen \u00E4r ofta drabbade. Det \u00E4r ocks\u00E5 vanligt att njurarna drabbas och om behandling inte s\u00E4tts in snabbt kan deras funktion kraftigt minska eller helt sl\u00E5s ut. Sjukdomen angriper dock inte endast dessa organ, utan hela kroppens blodomlopp kan drabbas och det \u00E4r s\u00E4rskilt de finare blodk\u00E4rlen (kapill\u00E4rerna) som angrips. Sjukdomen kan leda till subglottal stenos och granulombildningar i trachea eller under det subglottala rummet. Detta kan numera effektivt behandlas med laserkirurgi. I s\u00E4llsynta fall har man noterat fall med bl\u00F6dningar i hj\u00E4rnan och i tarmarna. Fall d\u00E4r vaskuliter upptr\u00E4tt p\u00E5 stora delar av huden f\u00F6rekommer ocks\u00E5. Utan behandling kan sjukdomen leda till d\u00F6den, men allvarligast nu f\u00F6r tiden \u00E4r att i synnerhet njurarna tar allvarlig skada. Granulomatos med polyangit \u00E4r en autoimmun sjukdom som inneb\u00E4r att kroppen producerar s.k. autoantikroppar som angriper blodk\u00E4rlen (i det h\u00E4r fallet) med inflammationer som f\u00F6ljd. I vanliga fall bildas antikroppar f\u00F6r att motverka exempelvis influensa och andra sjukdomar, men i fallet med autoantikroppar angrips kroppens egna och normala funktioner. Sjukdomsf\u00F6rloppet m\u00E4ts med hj\u00E4lp av dessa antikroppar som kallas C-ANCA. Behandling sker med kortison och cellgifter. Numera har man b\u00F6rjat behandlingar med humana antikroppar s\u00E5 kallade ANtiCD20-mediciner som Mabthera. Cirka 90 personer i Sverige insjuknar varje \u00E5r. Sjukdomen kan debutera i alla \u00E5ldrar, men vanligast \u00E4r i 50-60-\u00E5rs\u00E5ldern. Kvinnor och m\u00E4n drabbas i stort sett lika ofta. Antalet sjukdomsfall uppskattades 2008 till ungef\u00E4r 2200-2400 diagnostiserade fall. Sjukdomen har varit uppkallad efter Friedrich Wegener som i detalj beskrev den 1936 och 1939; den beskrevs dock f\u00F6rsta g\u00E5ngen 1897 av . Sjukdomen har f\u00E5tt ett nytt diagnosnamn Granulomatos med polyangit - (GPA). Sjukdomen kan ocks\u00E5 g\u00E5 under namnen: Klingers syndrom, Klinger-Wegeners syndrom, Wegeners sjukdom, Wegeners syndrom, Wegener-Churg-Klingers syndrom, eller Wegener-Klingers syndrom."@sv . . . "\u8089\u82BD\u816B\u4F75\u591A\u767C\u6027\u8840\u7BA1\u708E\uFF08Granulomatosis with polyangiitis\uFF0C\u7E2E\u5BEBGPA\uFF09\uFF0C\u820A\u7A31\u97CB\u683C\u7D0D\u8089\u82BD\u816B\uFF08\u82F1\u8A9E\uFF1AWegener's granulomatosis\uFF0C\u7E2E\u5BEB\u70BA WG\uFF09\uFF0C\u53C8\u8B6F\u4F5C\u83EF\u683C\u7D0D\u6C0F\u8089\u82BD\u816B\uFF0C\u662F\u4E00\u7A2E\u81EA\u9AD4\u514D\u75AB\u75BE\u75C5\uFF0C\u767C\u751F\u539F\u56E0\u4E0D\u660E\uFF0C\u7279\u5FB5\u70BA\u60E1\u6027\u7684\u8840\u7BA1\u708E\uFF0C\u4E3B\u8981\u4FB5\u72AF\u4E0A\u3001\u4E0B\u547C\u5438\u9053\u53CA\u814E\u81DF\uFF0C\u6703\u5F71\u97FF\u9F3B\u5B50\u3001\u80BA\u3001\u814E\u81DF\u4EE5\u53CA\u5176\u4ED6\u5668\u5B98\u3002"@zh . . . . . . . . . . . "\u0421\u0438\u043D\u0434\u0440\u043E\u0301\u043C \u0412\u0435\u0433\u0435\u043D\u0435\u0301\u0440\u0430 (\u0442\u0430\u043A\u043E\u0436 \u0433\u0440\u0430\u043D\u0443\u043B\u0435\u043C\u0430\u0442\u043E\u0301\u0437 \u0412\u0435\u0433\u0435\u043D\u0435\u0440\u0430, \u0430\u043D\u0433\u043B. Wegener's granulomatosis (WG); \u0433\u0440\u0430\u043D\u0443\u043B\u0435\u043C\u0430\u0442\u043E\u0437 \u0437 \u043F\u043E\u043B\u0456\u0430\u043D\u0433\u0456\u0457\u0442\u043E\u043C, \u0430\u043D\u0433\u043B. Granulomatosis with polyangiitis (GPA)) \u2014 \u0433\u0440\u0430\u043D\u0443\u043B\u0435\u043C\u0430\u0442\u043E\u0437\u043D\u043E-\u043D\u0435\u043A\u0440\u043E\u0442\u0438\u0447\u043D\u0438\u0439 \u0432\u0430\u0441\u043A\u0443\u043B\u0456\u0442 \u0437 \u043F\u0435\u0440\u0435\u0432\u0430\u0436\u043D\u0438\u043C \u0443\u0440\u0430\u0436\u0435\u043D\u043D\u044F\u043C \u0440\u0435\u0441\u043F\u0456\u0440\u0430\u0442\u043E\u0440\u043D\u043E\u0457 \u0441\u0438\u0441\u0442\u0435\u043C\u0438 \u0442\u0430 \u043D\u0438\u0440\u043E\u043A. \u0426\u0435\u0439 \u0441\u0438\u043D\u0434\u0440\u043E\u043C \u0447\u0430\u0441\u0442\u043E \u0440\u043E\u0437\u0433\u043B\u044F\u0434\u0430\u044E\u0442\u044C \u044F\u043A \u0432\u0430\u0440\u0456\u0430\u043D\u0442 \u0432\u0443\u0437\u043B\u0438\u043A\u043E\u0432\u043E\u0433\u043E \u043F\u0435\u0440\u0456\u0430\u0440\u0442\u0435\u0440\u0456\u0457\u0442\u0443."@uk . . . . "med"@en . . . . . "med"@en . . . . "\u0648\u0631\u0627\u0645 \u062D\u0628\u064A\u0628\u064A \u0648\u064A\u063A\u0646\u0631\u064A \u0623\u0648 \u062D\u0628\u064A\u0628\u0648\u0645 \u0648\u0627\u063A\u0646\u0631 \u0623\u0648 \u062F\u0627\u0621 \u0648\u0627\u063A\u0646\u0631 \u0627\u0644\u062D\u0628\u064A\u0628\u0648\u0645\u064A (\u0628\u0627\u0644\u0625\u0646\u062C\u0644\u064A\u0632\u064A\u0629: Wegener's granulomatosis)\u200F \u0647\u0648 \u0645\u0631\u0636 \u062C\u0647\u0627\u0632\u064A \u0645\u062C\u0647\u0648\u0644 \u0627\u0644\u0633\u0628\u0628 \u064A\u062A\u0638\u0627\u0647\u0631 \u0627\u0644\u062A\u0647\u0627\u0628\u064A\u0629 \u063A\u064A\u0631 \u0645\u062A\u062C\u0628\u0646\u0629 \u062D\u0648\u0644 \u0627\u0644\u0623\u0648\u0639\u064A\u0629\u060C \u0648\u0647\u0648 \u062F\u0627\u0621 \u0645\u062A\u0639\u062F\u062F \u0627\u0644\u0623\u062C\u0647\u0632\u0629 \u0642\u062F \u064A\u0624\u062B\u0631 \u0641\u064A \u0627\u0644\u062C\u0644\u062F \u0648\u0627\u0644\u0645\u0641\u0627\u0635\u0644\u060C \u062A\u0638\u0627\u0647\u0631\u0627\u062A\u0647 \u0627\u0644\u0643\u0644\u0648\u064A\u0629 \u0648\u0627\u0644\u0631\u0626\u0648\u064A\u0629 \u0645\u0647\u062F\u062F\u0629 \u0644\u0644\u062D\u064A\u0627\u0629\u060C \u0642\u062F \u064A\u0635\u064A\u0628 \u0623\u064A \u062C\u0632\u0621 \u0645\u0646 \u0627\u0644\u062C\u0647\u0627\u0632 \u0627\u0644\u062A\u0646\u0641\u0633\u064A. \u064A\u0639\u062A\u0645\u062F \u0627\u0644\u0639\u0644\u0627\u062C \u0639\u0644\u0649 \u0634\u062F\u0629 \u0627\u0644\u0645\u0631\u0636. \u064A\u064F\u0639\u0627\u0644\u062C \u0627\u0644\u062F\u0627\u0621 \u0627\u0644\u0634\u062F\u064A\u062F \u0639\u0627\u062F\u0629\u064B \u0628\u0625\u0634\u0631\u0627\u0643 \u0645\u062B\u0628\u0637\u0627\u062A \u0627\u0644\u0645\u0646\u0627\u0639\u0629 \u0645\u062B\u0644 \u0631\u064A\u062A\u0648\u0643\u0633\u064A\u0645\u0627\u0628 \u0623\u0648 \u0633\u064A\u0643\u0644\u0648\u0641\u0648\u0633\u0641\u0627\u0645\u064A\u062F \u0645\u0639 \u0627\u0644\u062C\u0631\u0639\u0627\u062A \u0627\u0644\u0639\u0627\u0644\u064A\u0629 \u0645\u0646 \u0627\u0644\u0633\u062A\u064A\u0631\u0648\u064A\u062F\u0627\u062A \u0627\u0644\u0642\u0634\u0631\u064A\u0629 \u0644\u0636\u0628\u0637 \u0627\u0644\u0623\u0639\u0631\u0627\u0636\u060C \u0648\u0622\u0632\u0627\u062B\u064A\u0648\u0628\u0631\u064A\u0646 \u0648\u0645\u064A\u062B\u0648\u062A\u0631\u064A\u0643\u0633\u0627\u062A \u0648\u0631\u064A\u062A\u0648\u0643\u0633\u064A\u0645\u0627\u0628 \u0644\u0644\u062D\u0641\u0627\u0638 \u0639\u0644\u0649 \u0627\u0644\u0647\u062C\u0648\u0639. \u064A\u064F\u0633\u062A\u062E\u062F\u0645 \u062A\u0628\u062F\u064A\u0644 \u0627\u0644\u0628\u0644\u0627\u0632\u0645\u0627 \u0641\u064A \u0627\u0644\u062D\u0627\u0644\u0627\u062A \u0627\u0644\u0634\u062F\u064A\u062F\u0629 \u0627\u0644\u062A\u064A \u062A\u062A\u0636\u0631\u0631 \u0641\u064A\u0647\u0627 \u0627\u0644\u0631\u0626\u0629 \u0648\u0627\u0644\u0643\u0644\u064A\u062A\u0627\u0646 \u0648\u0627\u0644\u0623\u0645\u0639\u0627\u0621."@ar . . "Granulomatose met polyangiitis (GPA), ook bekend als de ziekte van Wegener of granulomatose van Wegener, is een vorm van systeemvasculitis, een auto-immuunziekte. GPA wordt gekenmerkt door ontstekingen van de wanden van de kleine bloedvaten. Deze ontstekingen kunnen zich in meerdere organen manifesteren. De bloedvatontstekingen leiden tot versterf (necrose) van weefsels in organen. Tevens treden vrij karakteristieke ophopingen van ontstekingscellen (granulomen) op, met name in de neus en de longen, maar ook de nieren worden vaak aangetast, evenals de huid, ogen, gewrichten, centraal en perifeer zenuwstelsel en maag- en darmkanaal."@nl . "Die Granulomatose mit Polyangiitis (GPA) (fr\u00FCher Wegener-Granulomatose oder Morbus Wegener, benannt nach dem deutschen Pathologen Friedrich Wegener, Wegener-Klinger-Granulomatose, nach dem deutschen Pathologen Heinz Klinger) ist eine rheumatische Systemerkrankung des Gef\u00E4\u00DFsystems und gekennzeichnet durch eine nekrotisierende Entz\u00FCndung der Gef\u00E4\u00DFe (Vaskulitis) im Bereich des Kopfes, der Lunge und der Nieren, welche mit einer ulzerierenden Granulombildung der kleinen und mittleren Gef\u00E4\u00DFe in den oberen (Nase, Nasennebenh\u00F6hlen, Mittelohr, Oropharynx) und den unteren Atemwegen (Lunge) einhergeht. In 80 Prozent der F\u00E4lle kommt es zu einer Nierenk\u00F6rperchenentz\u00FCndung (Glomerulonephritis, genauer: Pauci-Immun-Glomerulonephritis als pathohistologisches Korrelat) und zur Bildung von Mikroaneurysmen i"@de . . . . "000135" . "D014890"@en . "Granulomatosis with polyangiitis (GPA), previously known as Wegener's granulomatosis (WG), is a rare long-term systemic disorder that involves the formation of granulomas and inflammation of blood vessels (vasculitis). It is a form of vasculitis that affects small- and medium-size vessels in many organs but most commonly affects the upper respiratory tract, lungs and kidneys. The signs and symptoms of GPA are highly varied and reflect which organs are supplied by the affected blood vessels. Typical signs and symptoms include nosebleeds, stuffy nose and crustiness of nasal secretions, and inflammation of the uveal layer of the eye. Damage to the heart, lungs and kidneys can be fatal. The cause of GPA is unknown. Genetics have been found to play a role in GPA though the risk of inheritance appears to be low. GPA treatment depends on the severity of the disease. Severe disease is typically treated with a combination of immunosuppressive medications such as rituximab or cyclophosphamide and high-dose corticosteroids to control the symptoms of the disease and azathioprine, methotrexate, or rituximab to keep the disease under control. Plasma exchange is also used in severe cases with damage to the lungs, kidneys, or intestines. The number of new cases of GPA each year is estimated to be 2.1\u201314.4 new cases per million people in Europe. GPA is rare in Japanese and African-American populations but occurs more often in people of Northern European descent. GPA is estimated to affect 3 cases per 100,000 people in the United States and equally affects men and women."@en . . . . . "La granulomatose avec polyang\u00E9ite (ou granulomatose de Wegener) est une maladie auto-immune qui a \u00E9t\u00E9 d\u00E9crite en 1939 par l'anatomopathologiste allemand Friedrich Wegener (1907\u20131990). Cette maladie est une vascularite syst\u00E9mique caract\u00E9ris\u00E9e par un aspect anatomopathologique de granulome et une localisation oto-rhino-laryngologique et pulmonaire pr\u00E9dominante. Cette vascularite atteint les petits et les moyens vaisseaux sanguins. Dans ce type de maladies, on trouve \u00E9galement : \n* le syndrome de Churg-Strauss, \n* la maladie de Beh\u00E7et, \n* la maladie de Kawasaki et \n* la ."@fr . . . . . . . . . . . "Granulomatosis with polyangiitis"@en . . "2401"^^ . . . . . . . . . . . . "Granulomatose mit Polyangiitis"@de . . . "\u0421\u0438\u043D\u0434\u0440\u043E\u0301\u043C \u0412\u0435\u0433\u0435\u043D\u0435\u0301\u0440\u0430 (\u0442\u0430\u043A\u043E\u0436 \u0433\u0440\u0430\u043D\u0443\u043B\u0435\u043C\u0430\u0442\u043E\u0301\u0437 \u0412\u0435\u0433\u0435\u043D\u0435\u0440\u0430, \u0430\u043D\u0433\u043B. Wegener's granulomatosis (WG); \u0433\u0440\u0430\u043D\u0443\u043B\u0435\u043C\u0430\u0442\u043E\u0437 \u0437 \u043F\u043E\u043B\u0456\u0430\u043D\u0433\u0456\u0457\u0442\u043E\u043C, \u0430\u043D\u0433\u043B. Granulomatosis with polyangiitis (GPA)) \u2014 \u0433\u0440\u0430\u043D\u0443\u043B\u0435\u043C\u0430\u0442\u043E\u0437\u043D\u043E-\u043D\u0435\u043A\u0440\u043E\u0442\u0438\u0447\u043D\u0438\u0439 \u0432\u0430\u0441\u043A\u0443\u043B\u0456\u0442 \u0437 \u043F\u0435\u0440\u0435\u0432\u0430\u0436\u043D\u0438\u043C \u0443\u0440\u0430\u0436\u0435\u043D\u043D\u044F\u043C \u0440\u0435\u0441\u043F\u0456\u0440\u0430\u0442\u043E\u0440\u043D\u043E\u0457 \u0441\u0438\u0441\u0442\u0435\u043C\u0438 \u0442\u0430 \u043D\u0438\u0440\u043E\u043A. \u0426\u0435\u0439 \u0441\u0438\u043D\u0434\u0440\u043E\u043C \u0447\u0430\u0441\u0442\u043E \u0440\u043E\u0437\u0433\u043B\u044F\u0434\u0430\u044E\u0442\u044C \u044F\u043A \u0432\u0430\u0440\u0456\u0430\u043D\u0442 \u0432\u0443\u0437\u043B\u0438\u043A\u043E\u0432\u043E\u0433\u043E \u043F\u0435\u0440\u0456\u0430\u0440\u0442\u0435\u0440\u0456\u0457\u0442\u0443."@uk . . . "La granulomatose avec polyang\u00E9ite (ou granulomatose de Wegener) est une maladie auto-immune qui a \u00E9t\u00E9 d\u00E9crite en 1939 par l'anatomopathologiste allemand Friedrich Wegener (1907\u20131990). Cette maladie est une vascularite syst\u00E9mique caract\u00E9ris\u00E9e par un aspect anatomopathologique de granulome et une localisation oto-rhino-laryngologique et pulmonaire pr\u00E9dominante. Cette vascularite atteint les petits et les moyens vaisseaux sanguins. Dans ce type de maladies, on trouve \u00E9galement : \n* le syndrome de Churg-Strauss, \n* la maladie de Beh\u00E7et, \n* la maladie de Kawasaki et \n* la ."@fr . . . . . . . . . . . . . . "Granulomat\u00F6s polyangit"@sv . "\u0413\u0440\u0430\u043D\u0443\u043B\u0435\u043C\u0430\u0442\u043E\u0301\u0437 \u0412\u0435\u0301\u0433\u0435\u043D\u0435\u0440\u0430 (\u0438\u0437\u0432\u0435\u0441\u0442\u0435\u043D \u0442\u0430\u043A\u0436\u0435 \u043A\u0430\u043A \u0433\u0440\u0430\u043D\u0443\u043B\u0435\u043C\u0430\u0442\u043E\u0301\u0437 \u0441 \u043F\u043E\u043B\u0438\u0430\u043D\u0433\u0438\u0438\u0301\u0442\u043E\u043C) \u2014 \u0430\u0443\u0442\u043E\u0438\u043C\u043C\u0443\u043D\u043D\u043E\u0435 \u0433\u0440\u0430\u043D\u0443\u043B\u0451\u043C\u0430\u0442\u043E\u0437\u043D\u043E\u0435 \u0432\u043E\u0441\u043F\u0430\u043B\u0435\u043D\u0438\u0435 \u0441\u0442\u0435\u043D\u043E\u043A \u0441\u043E\u0441\u0443\u0434\u043E\u0432 (\u0432\u0430\u0441\u043A\u0443\u043B\u0438\u0442), \u0437\u0430\u0445\u0432\u0430\u0442\u044B\u0432\u0430\u044E\u0449\u0435\u0435 \u043C\u0435\u043B\u043A\u0438\u0435 \u0438 \u0441\u0440\u0435\u0434\u043D\u0438\u0435 \u043A\u0440\u043E\u0432\u0435\u043D\u043E\u0441\u043D\u044B\u0435 \u0441\u043E\u0441\u0443\u0434\u044B: \u043A\u0430\u043F\u0438\u043B\u043B\u044F\u0440\u044B, \u0432\u0435\u043D\u0443\u043B\u044B, \u0430\u0440\u0442\u0435\u0440\u0438\u043E\u043B\u044B \u0438 \u0430\u0440\u0442\u0435\u0440\u0438\u0438, \u0441 \u0432\u043E\u0432\u043B\u0435\u0447\u0435\u043D\u0438\u0435\u043C \u0432\u0435\u0440\u0445\u043D\u0438\u0445 \u0434\u044B\u0445\u0430\u0442\u0435\u043B\u044C\u043D\u044B\u0445 \u043F\u0443\u0442\u0435\u0439, \u0433\u043B\u0430\u0437, \u043F\u043E\u0447\u0435\u043A, \u043B\u0451\u0433\u043A\u0438\u0445 \u0438 \u0434\u0440\u0443\u0433\u0438\u0445 \u043E\u0440\u0433\u0430\u043D\u043E\u0432. \u041E\u0442\u043D\u043E\u0441\u0438\u0442\u0441\u044F \u043A \u0441\u0438\u0441\u0442\u0435\u043C\u043D\u044B\u043C \u0410\u041D\u0426\u0410-\u0430\u0441\u0441\u043E\u0446\u0438\u0438\u0440\u043E\u0432\u0430\u043D\u043D\u044B\u043C \u043D\u0435\u043A\u0440\u043E\u0442\u0438\u0437\u0438\u0440\u0443\u044E\u0449\u0438\u043C \u0432\u0430\u0441\u043A\u0443\u043B\u0438\u0442\u0430\u043C."@ru . . "Granulomatose avec polyang\u00E9ite"@fr . "\uB2E4\uBC1C\uD608\uAD00\uC5FC \uB3D9\uBC18 \uC721\uC544\uC885\uC99D"@ko . . "Wegener's granulomatosis"@en . . . . . . . "Granulomatosis con poliangitis"@es . . . . . "Granulomatose com poliangiite"@pt . "\u0648\u0631\u0627\u0645 \u062D\u0628\u064A\u0628\u064A \u0648\u064A\u063A\u0646\u0631\u064A \u0623\u0648 \u062D\u0628\u064A\u0628\u0648\u0645 \u0648\u0627\u063A\u0646\u0631 \u0623\u0648 \u062F\u0627\u0621 \u0648\u0627\u063A\u0646\u0631 \u0627\u0644\u062D\u0628\u064A\u0628\u0648\u0645\u064A (\u0628\u0627\u0644\u0625\u0646\u062C\u0644\u064A\u0632\u064A\u0629: Wegener's granulomatosis)\u200F \u0647\u0648 \u0645\u0631\u0636 \u062C\u0647\u0627\u0632\u064A \u0645\u062C\u0647\u0648\u0644 \u0627\u0644\u0633\u0628\u0628 \u064A\u062A\u0638\u0627\u0647\u0631 \u0627\u0644\u062A\u0647\u0627\u0628\u064A\u0629 \u063A\u064A\u0631 \u0645\u062A\u062C\u0628\u0646\u0629 \u062D\u0648\u0644 \u0627\u0644\u0623\u0648\u0639\u064A\u0629\u060C \u0648\u0647\u0648 \u062F\u0627\u0621 \u0645\u062A\u0639\u062F\u062F \u0627\u0644\u0623\u062C\u0647\u0632\u0629 \u0642\u062F \u064A\u0624\u062B\u0631 \u0641\u064A \u0627\u0644\u062C\u0644\u062F \u0648\u0627\u0644\u0645\u0641\u0627\u0635\u0644\u060C \u062A\u0638\u0627\u0647\u0631\u0627\u062A\u0647 \u0627\u0644\u0643\u0644\u0648\u064A\u0629 \u0648\u0627\u0644\u0631\u0626\u0648\u064A\u0629 \u0645\u0647\u062F\u062F\u0629 \u0644\u0644\u062D\u064A\u0627\u0629\u060C \u0642\u062F \u064A\u0635\u064A\u0628 \u0623\u064A \u062C\u0632\u0621 \u0645\u0646 \u0627\u0644\u062C\u0647\u0627\u0632 \u0627\u0644\u062A\u0646\u0641\u0633\u064A. \u064A\u0639\u062A\u0645\u062F \u0627\u0644\u0639\u0644\u0627\u062C \u0639\u0644\u0649 \u0634\u062F\u0629 \u0627\u0644\u0645\u0631\u0636. \u064A\u064F\u0639\u0627\u0644\u062C \u0627\u0644\u062F\u0627\u0621 \u0627\u0644\u0634\u062F\u064A\u062F \u0639\u0627\u062F\u0629\u064B \u0628\u0625\u0634\u0631\u0627\u0643 \u0645\u062B\u0628\u0637\u0627\u062A \u0627\u0644\u0645\u0646\u0627\u0639\u0629 \u0645\u062B\u0644 \u0631\u064A\u062A\u0648\u0643\u0633\u064A\u0645\u0627\u0628 \u0623\u0648 \u0633\u064A\u0643\u0644\u0648\u0641\u0648\u0633\u0641\u0627\u0645\u064A\u062F \u0645\u0639 \u0627\u0644\u062C\u0631\u0639\u0627\u062A \u0627\u0644\u0639\u0627\u0644\u064A\u0629 \u0645\u0646 \u0627\u0644\u0633\u062A\u064A\u0631\u0648\u064A\u062F\u0627\u062A \u0627\u0644\u0642\u0634\u0631\u064A\u0629 \u0644\u0636\u0628\u0637 \u0627\u0644\u0623\u0639\u0631\u0627\u0636\u060C \u0648\u0622\u0632\u0627\u062B\u064A\u0648\u0628\u0631\u064A\u0646 \u0648\u0645\u064A\u062B\u0648\u062A\u0631\u064A\u0643\u0633\u0627\u062A \u0648\u0631\u064A\u062A\u0648\u0643\u0633\u064A\u0645\u0627\u0628 \u0644\u0644\u062D\u0641\u0627\u0638 \u0639\u0644\u0649 \u0627\u0644\u0647\u062C\u0648\u0639. \u064A\u064F\u0633\u062A\u062E\u062F\u0645 \u062A\u0628\u062F\u064A\u0644 \u0627\u0644\u0628\u0644\u0627\u0632\u0645\u0627 \u0641\u064A \u0627\u0644\u062D\u0627\u0644\u0627\u062A \u0627\u0644\u0634\u062F\u064A\u062F\u0629 \u0627\u0644\u062A\u064A \u062A\u062A\u0636\u0631\u0631 \u0641\u064A\u0647\u0627 \u0627\u0644\u0631\u0626\u0629 \u0648\u0627\u0644\u0643\u0644\u064A\u062A\u0627\u0646 \u0648\u0627\u0644\u0623\u0645\u0639\u0627\u0621. \u064A\u064F\u0642\u062F\u0631 \u0639\u062F\u062F \u0627\u0644\u062D\u0627\u0644\u0627\u062A \u0627\u0644\u062C\u062F\u064A\u062F\u0629 \u0633\u0646\u0648\u064A\u064B\u0627 \u0628\u064A\u0646 2.1-14.4 \u0644\u0643\u0644 \u0645\u0644\u064A\u0648\u0646 \u0634\u062E\u0635 \u0641\u064A \u0623\u0648\u0631\u0648\u0628\u0627. \u064A\u0646\u062F\u0631 \u0638\u0647\u0648\u0631 \u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 \u0644\u062F\u0649 \u0627\u0644\u064A\u0627\u0628\u0627\u0646\u064A\u064A\u0646 \u0648\u0627\u0644\u0623\u0645\u0631\u064A\u0643\u064A\u064A\u0646 \u0627\u0644\u0623\u0641\u0627\u0631\u0642\u0629\u060C \u0644\u0643\u0646\u0647 \u064A\u0634\u064A\u0639 \u0628\u064A\u0646 \u0627\u0644\u0645\u0646\u062D\u062F\u0631\u064A\u0646 \u0645\u0646 \u0623\u0635\u0648\u0644 \u0634\u0645\u0627\u0644 \u0623\u0648\u0631\u0648\u0628\u064A\u0629. \u064A\u064F\u0642\u062F\u0631 \u0623\u0646 \u0648\u0631\u0627\u0645 \u0648\u0627\u063A\u0646\u0631 \u0627\u0644\u062D\u0628\u064A\u0628\u064A \u064A\u0635\u064A\u0628 3 \u0645\u0646 \u0628\u064A\u0646 \u0643\u0644 100,000 \u0634\u062E\u0635 \u0641\u064A \u0627\u0644\u0648\u0644\u0627\u064A\u0627\u062A \u0627\u0644\u0645\u062A\u062D\u062F\u0629\u060C \u0648\u062A\u062A\u0633\u0627\u0648\u0649 \u0646\u0633\u0628 \u0627\u0644\u0625\u0635\u0627\u0628\u0629 \u0628\u064A\u0646 \u0627\u0644\u0631\u062C\u0627\u0644 \u0648\u0627\u0644\u0646\u0633\u0627\u0621."@ar . . "135"^^ . . . . . . . . "Granulomatosis Wegener atau dikenal juga dengan granulomatosis dengan poliangitiis (GPA) adalah gangguan sistemik yang melibatkan dan . Kondisi ini terlihat dari inflamasi pembuluh darah yang melibatkan pembuluh kecil dan sedang di berbagai organ penting. Inflamasi di daerah paru dan ginjal bisa berakibat fatal. Penanganannya bisa dilakukan dengan melakukan supresi imunitas. \n* l \n* \n* s"@in . . . . "\u0421\u0438\u043D\u0434\u0440\u043E\u043C \u0412\u0435\u0433\u0435\u043D\u0435\u0440\u0430"@uk . "\u591A\u767A\u8840\u7BA1\u708E\u6027\u8089\u82BD\u816B\u75C7\uFF08\u305F\u306F\u3064\u3051\u3063\u304B\u3093\u3048\u3093\u305B\u3044\u306B\u304F\u3052\u3057\u3085\u3057\u3087\u3046\u3001\u82F1\u8A9E: Granulomatosis with polyangiitis; GPA\uFF09\u306F1939\u5E74\u30C9\u30A4\u30C4\u306E\u75C5\u7406\u5B66\u8005Wegener\u306B\u3088\u308A\u5831\u544A\u3055\u308C\u305F\u3002\u304B\u3064\u3066\u306F\u3001\u30A6\u30A7\u30B2\u30CA\u30FC\u8089\u82BD\u816B\u75C7 (\u30A6\u30A7\u30B2\u30CA\u30FC\u306B\u304F\u3052\u3057\u3085\u3057\u3087\u3046\u3001\u82F1\u8A9E: Wegener's granulomatosis) \u3068\u306E\u540D\u79F0\u304C\u983B\u7528\u3055\u308C\u3066\u3044\u305F\u304C\u3001\u8840\u7BA1\u708E\u306E\u5206\u985E\u3092\u5B9A\u3081\u305FCHCC\u5206\u985E\u304C2012\u5E74\u306B\u6539\u8A02\u3055\u308C\u3001DHCC\u5206\u985E\u540D\u79F0\u306F\u300C\u591A\u767A\u8840\u7BA1\u708E\u6027\u8089\u82BD\u816B\u75C7 (Granulomatosis with polyangiitis)\u300D\u3068\u306A\u3063\u3066\u3044\u308B\u3002 \u5168\u8EAB\u6027\u306E\u8840\u7BA1\u708E\u3067\u3001\u4E2D - \u5C0F\u578B\u52D5\u8108\u3092\u50B7\u5BB3\u3059\u308B\u75BE\u60A3\u3002 \u9F3B\u3084\u306E\u3069\u306E\u50B7\u5BB3\u304B\u3089\u306F\u3058\u307E\u308B\u306E\u3067\u6700\u521D\u306F\u98A8\u90AA\u306E\u3088\u3046\u3067\u3082\u3042\u308B\u304C\u3001\u6025\u901F\u306B\u9593\u8CEA\u6027\u80BA\u708E\u3001\u6025\u901F\u9032\u884C\u6027\u7CF8\u7403\u4F53\u814E\u708E\u3092\u304D\u305F\u3059\u3002\u3057\u305F\u304C\u3063\u3066\u75C7\u72B6\u306F\u3001\u54B3\u3001\u547C\u5438\u56F0\u96E3\u3001\u6D6E\u816B\u306A\u3069\u3067\u3042\u308B\u3002\u8EFD\u5EA6\u306E\u767A\u71B1\u3082\u304A\u3053\u308B\u3002\u9F3B\u306B\u95A2\u3057\u3066\u3082\u5185\u90E8\u69CB\u9020\u304C\u7834\u58CA\u3055\u308C\u3001\u3064\u3076\u308C\u3066\u3092\u5448\u3059\u308B\u3053\u3068\u304C\u3042\u308B\u3002\u3001\u3076\u3069\u3046\u819C\u708E\u3001\u89D2\u819C\u6F70\u760D\u306A\u3069\u773C\u79D1\u7684\u75BE\u60A3\u3082\u8D77\u3053\u308B\u3053\u3068\u304C\u3042\u308B\u3002\u305D\u306E\u307B\u304B\u76AE\u819A\uFF08\u6709\u75DB\u6027\u7D05\u6591\uFF09\u3001\u795E\u7D4C\u3001\u8133\u3092\u304A\u304B\u3057\u3046\u308B\u3002 \u8840\u6DB2\u691C\u67FB\u3067\u306Fc-ANCA\uFF08PR3-ANCA\uFF09\u304C\u7279\u7570\u7684\u306B\u4E0A\u6607\u3059\u308B\u3002\u30B9\u30C6\u30ED\u30A4\u30C9\u5264\u306A\u3069\u306E\u6CBB\u7642\u3092\u3082\u3063\u3066\u3057\u3066\u3082\u304D\u308F\u3081\u3066\u91CD\u7BE4\u306A\u75BE\u60A3\u3067\u3042\u308B\u3002"@ja . . . . . . . . . "14057" . "\uB2E4\uBC1C\uD608\uAD00\uC5FC \uB3D9\uBC18 \uC721\uC544\uC885\uC99D(granulomatosis with polyangiitis; GPA) \uB610\uB294 \uBCA0\uAC8C\uB108 \uC721\uC544\uC885\uC99D(Wegener's granulomatosis; WG)\uC740 \uACFC \uC721\uC544\uC885\uC774 \uB3D9\uC2DC\uC5D0 \uB098\uD0C0\uB098\uB294 \uC870\uC9C1\uC7A5\uC560\uC774\uB2E4. \uD5C8\uD30C\uC640 \uC2E0\uC7A5\uC5D0 \uC190\uC0C1\uC744 \uC785\uD788\uBA70, \uC774 \uC190\uC0C1\uC740 \uB9E4\uC6B0 \uCE58\uBA85\uC801\uC774\uC5B4\uC11C \uC0DD\uBA85\uC744 \uC704\uD611\uD560 \uC218 \uC788\uB2E4. \uB9CC\uC131\uC801\uC778 \uBA74\uC5ED\uC5B5\uC81C\uB85C \uBC1C\uC0DD\uD560 \uC218 \uC788\uB2E4. \"\uBCA0\uAC8C\uB108 \uC721\uC544\uC885\"\uC774\uB780 \uBA85\uCE6D\uC740 1936\uB144 \uBCD1\uC744 \uBC1C\uACAC\uD55C \uC758 \uC774\uB984\uC774 \uBD99\uC740 \uAC83\uC774\uB2E4. 2000\uB144 \uBCA0\uAC8C\uB108\uAC00 \uB098\uCE58 \uB2F9\uC6D0\uC774\uC5C8\uC74C\uC774 \uBC1D\uD600\uC9C0\uC790 \uBCA0\uAC8C\uB108\uC758 \uC774\uB984\uC744 \uC5B8\uAE09\uD558\uB294 \uAC83\uC774 \uD130\uBD80\uC2DC\uB418\uC5B4 \uD604\uC7AC\uC758 \uC774\uB984\uC774 \uC0C8\uB85C \uBD99\uC5C8\uB2E4."@ko . . . . "Granulomatose com poliangiite, anteriormente denominada Granulomatose de Wegener ou doen\u00E7a de Wegener, \u00E9 uma rara doen\u00E7a autoimune, ou seja, uma doen\u00E7a que ataca elementos constitutivos normais do corpo humano, fazendo com que nossos anticorpos ataquem a n\u00F3s mesmos. \u00C9 importante ressaltar que a denomina\u00E7\u00E3o anterior de granulomatose de Wegener prestigiava Friederich Wegener, m\u00E9dico alem\u00E3o ardoroso filiado ao partido nazista, grande admirador de Hitler e com amplo conhecimento das atrocidades contra judeus e outras minorias. A Granulomatose com poliangiite \u00E9 uma forma de vasculite, que \u00E9 uma inflama\u00E7\u00E3o dos vasos sangu\u00EDneos, provocada pelo pr\u00F3prio sistema imunol\u00F3gico, afetando principalmente rins e pulm\u00F5es, apesar de eventualmente atingir outros \u00F3rg\u00E3os."@pt . "Granulomatosis Wegener"@in . . . "446.4" . . "\u0397 \u03BA\u03BF\u03BA\u03BA\u03B9\u03C9\u03BC\u03B1\u03C4\u03CE\u03B4\u03B7\u03C2 \u03B1\u03B3\u03B3\u03B5\u03B9\u03AF\u03C4\u03B9\u03B4\u03B1 \u0392\u03AD\u03B3\u03BA\u03B5\u03BD\u03B5\u03C1 \u03B5\u03AF\u03BD\u03B1\u03B9 \u03BC\u03AF\u03B1 \u03C3\u03C0\u03AC\u03BD\u03B9\u03B1\u03C2 \u03C3\u03C5\u03C3\u03C4\u03B7\u03BC\u03B1\u03C4\u03B9\u03BA\u03AE \u03B1\u03B3\u03B3\u03B5\u03B9\u03AF\u03C4\u03B9\u03B4\u03B1 \u03C4\u03C9\u03BD \u03BC\u03B9\u03BA\u03C1\u03BF\u03CD \u03BC\u03B5\u03B3\u03AD\u03B8\u03BF\u03C5\u03C2 \u03B1\u03B3\u03B3\u03B5\u03AF\u03C9\u03BD \u03C4\u03BF\u03C5 \u03B1\u03AF\u03BC\u03B1\u03C4\u03BF\u03C2 \u03C0.\u03C7. \u03C6\u03BB\u03B5\u03B2\u03AF\u03B4\u03B9\u03B1, \u03B1\u03C1\u03C4\u03B7\u03C1\u03AF\u03B4\u03B9\u03B1 \u03BA\u03B1\u03B9 \u03C4\u03C1\u03B9\u03C7\u03BF\u03B5\u03B9\u03B4\u03AE. \u03A0\u03C1\u03BF\u03C3\u03B2\u03AC\u03BB\u03BB\u03B5\u03B9 \u03C4\u03BF \u03B1\u03BD\u03CE\u03C4\u03B5\u03C1\u03BF \u03B1\u03BD\u03B1\u03C0\u03BD\u03B5\u03C5\u03C3\u03C4\u03B9\u03BA\u03CC \u03C3\u03CD\u03C3\u03C4\u03B7\u03BC\u03B1 (\u03BC\u03CD\u03C4\u03B7, \u03C3\u03C4\u03CC\u03BC\u03B1, \u03C6\u03AC\u03C1\u03C5\u03B3\u03B3\u03B1, \u03BB\u03AC\u03C1\u03C5\u03B3\u03B3\u03B1, \u03C4\u03C1\u03B1\u03C7\u03B5\u03AF\u03B1, \u03B2\u03C1\u03CC\u03B3\u03C7\u03BF\u03B9), \u03C4\u03BF \u03BA\u03B1\u03C4\u03CE\u03C4\u03B5\u03C1\u03BF \u03B1\u03BD\u03B1\u03C0\u03BD\u03B5\u03C5\u03C3\u03C4\u03B9\u03BA\u03CC (\u03C0\u03BD\u03B5\u03CD\u03BC\u03BF\u03BD\u03B5\u03C2, \u03BD\u03B5\u03C6\u03C1\u03BF\u03CD\u03C2) \u03BA\u03B1\u03B8\u03CE\u03C2 \u03B5\u03C0\u03AF\u03C3\u03B7\u03C2 \u03BA\u03B1\u03B9 \u03AC\u03BB\u03BB\u03B1 \u03CC\u03C1\u03B3\u03B1\u03BD\u03B1. \u0394\u03B9\u03B1\u03BA\u03C1\u03AF\u03BD\u03B5\u03C4\u03B1\u03B9 \u03C3\u03B5 \u03B4\u03CD\u03BF \u03C4\u03CD\u03C0\u03BF\u03C5\u03C2 \u03B1\u03BD\u03AC\u03BB\u03BF\u03B3\u03B1 \u03BC\u03B5 \u03C4\u03B7\u03BD \u03C0\u03C1\u03BF\u03C3\u03B2\u03BF\u03BB\u03AE \u03BA\u03B1\u03B9 \u03C4\u03B7\u03BD \u03B5\u03BE\u03AC\u03C0\u03BB\u03C9\u03C3\u03AE \u03C4\u03BF\u03C5\u03C2 \u03C3\u03C4\u03BF\u03BD \u03BF\u03C1\u03B3\u03B1\u03BD\u03B9\u03C3\u03BC\u03CC."@el . . "M31.3" . "Micrograph showing features characteristic of granulomatosis with polyangiitis \u2013 a vasculitis and granulomas with multi-nucleated giant cells. H&E stain."@en . . . .