. . . . . . "D\u00E9ficit en 3-hydroxyacyl-coenzyme A d\u00E9shydrog\u00E9nase des acides gras \u00E0 cha\u00EEne longue"@fr . . . . . . . . . . . "Long-chain 3-hydroxyacyl-coenzyme; A dehydrogenase deficiency has an autosomal recessive pattern of inheritance."@en . . . . "1284"@en . . . . "Le d\u00E9ficit en 3-hydroxyacyl-coenzyme A d\u00E9shydrog\u00E9nase des acides gras \u00E0 cha\u00EEne longue, souvent abr\u00E9g\u00E9 en d\u00E9ficit en LCHAD, est l'une des maladies rares \u00E0 transmission autosomique r\u00E9cessive li\u00E9 \u00E0 l'oxydation des acides gras qui emp\u00EAche le corps de convertir certaines graisses en \u00E9nergie. Cela peut \u00EAtre dangereux, en particulier pendant les p\u00E9riodes de je\u00FBne."@fr . "Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency"@en . "600890"^^ . . . . "Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency"@en . "Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency is a rare autosomal recessive fatty acid oxidation disorder that prevents the body from converting certain fats into energy. This can become life-threatening, particularly during periods of fasting."@en . "277.85" . . . . . . "Le d\u00E9ficit en 3-hydroxyacyl-coenzyme A d\u00E9shydrog\u00E9nase des acides gras \u00E0 cha\u00EEne longue, souvent abr\u00E9g\u00E9 en d\u00E9ficit en LCHAD, est l'une des maladies rares \u00E0 transmission autosomique r\u00E9cessive li\u00E9 \u00E0 l'oxydation des acides gras qui emp\u00EAche le corps de convertir certaines graisses en \u00E9nergie. Cela peut \u00EAtre dangereux, en particulier pendant les p\u00E9riodes de je\u00FBne."@fr . . . . . . . "1084520391"^^ . "ped"@en . . . ""@en . . "1284"^^ . "1557100"^^ . . . . . "277.85"^^ . . . . . . "Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency is a rare autosomal recessive fatty acid oxidation disorder that prevents the body from converting certain fats into energy. This can become life-threatening, particularly during periods of fasting."@en . . . . . . "LCHAD deficiency"@en . . . "ped"@en . . . . . "Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency"@en . . . . "4163"^^ . . "600890"^^ . . . . . . . . .