. . . . . . . . . . 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"Espectrina"@es . . . . . . . . "Spectrin is a cytoskeletal protein that lines the intracellular side of the plasma membrane in eukaryotic cells. Spectrin forms pentagonal or hexagonal arrangements, forming a scaffold and playing an important role in maintenance of plasma membrane integrity and cytoskeletal structure. The hexagonal arrangements are formed by tetramers of spectrin subunits associating with short actin filaments at either end of the tetramer. These short actin filaments act as junctional complexes allowing the formation of the hexagonal mesh. The protein is named spectrin since it was first isolated as a major protein component of human red blood cells which had been treated with mild detergents; the detergents lysed the cells and the hemoglobin and other cytoplasmic components were washed out. In the light"@en . "Spektrin je velk\u00FD protein tvo\u0159\u00EDc\u00ED sou\u010D\u00E1st cytoskelet\u00E1rn\u00ED s\u00EDt\u011B pod plazmatickou membr\u00E1nou. Udr\u017Euje tvar a pru\u017Enost t\u00E9to membr\u00E1ny. V aminokyselinov\u00E9 sekvenci se nach\u00E1z\u00ED 106 tzv. , kter\u00E9 umo\u017E\u0148uj\u00ED zaujmout strukturu pru\u017En\u00E9 . Spektrin \u03B1 a \u03B2 spolu nav\u00EDc tvo\u0159\u00ED heterodimer a d\u00E1le agreguj\u00ED do rozs\u00E1hl\u00FDch polymer\u016F obep\u00EDnaj\u00EDc\u00EDch celou bu\u0148ku."@cs . . . "Spektrin je velk\u00FD protein tvo\u0159\u00EDc\u00ED sou\u010D\u00E1st cytoskelet\u00E1rn\u00ED s\u00EDt\u011B pod plazmatickou membr\u00E1nou. Udr\u017Euje tvar a pru\u017Enost t\u00E9to membr\u00E1ny. V aminokyselinov\u00E9 sekvenci se nach\u00E1z\u00ED 106 tzv. , kter\u00E9 umo\u017E\u0148uj\u00ED zaujmout strukturu pru\u017En\u00E9 . Spektrin \u03B1 a \u03B2 spolu nav\u00EDc tvo\u0159\u00ED heterodimer a d\u00E1le agreguj\u00ED do rozs\u00E1hl\u00FDch polymer\u016F obep\u00EDnaj\u00EDc\u00EDch celou bu\u0148ku."@cs . . . "\u30B9\u30DA\u30AF\u30C8\u30EA\u30F3"@ja . . 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"L'espectrina \u00E9s una prote\u00EFna del citoesquelet que cobreix la part intracel\u00B7lular de la membrana plasm\u00E0tica de molts tipus de c\u00E8l\u00B7lules adoptant disposicions pentagonals o hexagonals, donant suport estructural i jugant un paper important en el manteniment de la integritat de la membrana plasm\u00E0tica i de l'estructura del citoesquelet. Les disposicions hexagonals s\u00F3n formades per tetr\u00E0mers d'espectrina associades a curts filaments d'actina en els extrems del tetr\u00E0mer. Aquests curts filaments d'actina actuen com complexos d'uni\u00F3 permetent la formaci\u00F3 de la xarxa hexagonal."@ca . . . . . . "La espectrina es una de las prote\u00EDnas m\u00E1s importantes del eritrocito. Su nombre se debe a que si introducimos gl\u00F3bulos rojos en un medio hipot\u00F3nico \u00E9stos absorben agua y se acaban lisando (estallando). Al lisarse, la hemoglobina sale al exterior de la c\u00E9lula quedando s\u00F3lo la membrana, lo que recibe el nombre de \"fantasma de eritrocito\". Una de las prote\u00EDnas del fantasma es la espectrina, y de ah\u00ED le viene el nombre."@es . . . . . . . . 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"Spectrin"@en . "2864344"^^ . . "Espektrina"@eu . . . . . . "La espectrina es una de las prote\u00EDnas m\u00E1s importantes del eritrocito. Su nombre se debe a que si introducimos gl\u00F3bulos rojos en un medio hipot\u00F3nico \u00E9stos absorben agua y se acaban lisando (estallando). Al lisarse, la hemoglobina sale al exterior de la c\u00E9lula quedando s\u00F3lo la membrana, lo que recibe el nombre de \"fantasma de eritrocito\". Una de las prote\u00EDnas del fantasma es la espectrina, y de ah\u00ED le viene el nombre."@es . . . . . . . . . "La spettrina \u00E8 una proteina citoscheletrica presente sul versante interno della membrana citoplasmatica delle cellule eucariotiche. Isolata per la prima volta dagli eritrociti, riveste un ruolo importante nel mantenimento dell'integrit\u00E0 della membrana plasmatica e struttura citoscheletrica. Mutazioni che coinvolgono la spettrina comunemente causano difetti ereditari dell'eritrocita, tra cui ellissocitosi ereditaria e sferocitosi ereditaria."@it . . . 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"\u8840\u5F71\u86CB\u767D\uFF08Spectrin\uFF09\uFF0C\u4E00\u7A2E\u7D30\u80DE\u7D50\u69CB\u86CB\u767D\uFF0C\u5927\u591A\u4F4D\u65BC\u7D05\u8840\u7403\u7D30\u80DE\u819C\u5167\u5074\uFF0C\u662F\u7D05\u8840\u7403\u9AA8\u67B6\u7684\u4E3B\u8981\u6210\u5206\u3002\u8840\u5F71\u86CB\u767D\u5728\u6574\u500B\u7D30\u80DE\u819C\u5167\u5074\u5F62\u6210\u53EF\u8B8A\u5F62\u7684\u67B6\u69CB\uFF0C\u4EE5\u7DAD\u6301\u7D05\u8840\u7403\u7684\u96D9\u51F9\u5713\u76E4\u69CB\u9020\u3002\u8840\u5F71\u86CB\u767D\u5F62\u6210\u4E94\u8FB9\u5F62\u6216\u516D\u8FB9\u5F62\u6392\u5217\uFF0C\u5F62\u6210\u652F\u67B6\u5E76\u5728\u7EF4\u6301\u7EC6\u80DE\u819C\u5B8C\u6574\u6027\u548C\u7EC6\u80DE\u9AA8\u67B6\u7ED3\u6784\u4E2D\u8D77\u91CD\u8981\u4F5C\u7528\u3002\u516D\u89D2\u5F62\u6392\u5217\u7531\u8840\u5F71\u86CB\u767D\u4E9A\u57FA\u7684\u56DB\u805A\u4F53\u5F62\u6210\uFF0C\u6240\u8FF0\u56DB\u805A\u4F53\u4E0E\u56DB\u805A\u4F53\u4E24\u7AEF\u7684\u77ED\u808C\u52A8\u86CB\u767D\u4E1D\u76F8\u5173\u8054\u3002 \u8FD9\u4E9B\u77ED\u7684\u808C\u52A8\u86CB\u767D\u4E1D\u5145\u5F53\u8FDE\u63A5\u590D\u5408\u7269\uFF0C\u5F97\u4EE5\u5F62\u6210\u516D\u8FB9\u5F62\u7F51\u3002 \u8BE5\u86CB\u767D\u8D28\u88AB\u547D\u540D\u4E3A\u8840\u5F71\u86CB\u767D\uFF0C\u56E0\u4E3A\u5B83\u9996\u5148\u4F5C\u4E3A\u4EBA\u7C7B\u7EA2\u7EC6\u80DE\u7684\u4E3B\u8981\u86CB\u767D\u8D28\u6210\u5206\u88AB\u5206\u79BB\u51FA\u6765\uFF0C\u540E\u8005\u5DF2\u7ECF\u7528\u6E29\u548C\u7684\u6D17\u6DA4\u5242\u5904\u7406\u8FC7; \u6D17\u6DA4\u5242\u88C2\u89E3\u7EC6\u80DE\uFF0C\u8840\u7EA2\u86CB\u767D\u548C\u5176\u4ED6\u7EC6\u80DE\u8D28\u6210\u5206\u88AB\u6D17\u6389\u3002 \u5B83\u662F\u4E00\u7A2E\u9577\u4E14\u5177\u6709\u4F38\u7E2E\u6027\u7684\u7E96\u7DAD\u72C0\u86CB\u767D\uFF0C\u9577\u7D04100nm\uFF0C\u7531\u5169\u689D\u55AE\u9AD4\uFF1A\u03B1I\u3001\u03B2I\u5148\u5E73\u884C\u6392\u5217\u7D50\u5408\u6210\u4E8C\u805A\u9AD4\uFF0C\u5169\u500B\u4E8C\u805A\u9AD4\u518D\u4EE5\u982D\u5C0D\u982D\u7684\u65B9\u5F0F\u9023\u63A5\u6210200nm\u9577\u7684\u56DB\u805A\u9AD4\u30025\u52306\u500B\u56DB\u805A\u9AD4\u7684\u5C3E\u7AEF\u900F\u904Eprotein4.1\u3001protein4.2\u3001protein4.9\u3001\u808C\u52D5\u86CB\u767D\uFF08actin\uFF09\u3001\u9328\u5B9A\u86CB\u767D\uFF08ankyrin\uFF09\u7B49\u7B49\u86CB\u767D\u8CEA\u7684\u5E6B\u52A9\u4E0B\uFF0C\u56FA\u5B9A\u5728\u67D0\u4E9B\u8DE8\u819C\u86CB\u767D\uFF08intergral membrane proteins\uFF09\u4E0A\u3002"@zh . . . . . . . . "Spektrin"@cs . . . . . . . . . . "Spettrina"@it . "\u0421\u043F\u0435\u043A\u0442\u0440\u0438\u043D \u2014 \u044D\u0442\u043E \u0431\u0435\u043B\u043E\u043A \u0446\u0438\u0442\u043E\u0441\u043A\u0435\u043B\u0435\u0442\u0430, \u043A\u043E\u0442\u043E\u0440\u044B\u0439 \u0432\u044B\u0441\u0442\u0438\u043B\u0430\u0435\u0442 \u0432\u043D\u0443\u0442\u0440\u0435\u043D\u043D\u044E\u044E \u0441\u0442\u043E\u0440\u043E\u043D\u0443 \u043F\u043B\u0430\u0437\u043C\u0430\u0442\u0438\u0447\u0435\u0441\u043A\u043E\u0439 \u043C\u0435\u043C\u0431\u0440\u0430\u043D\u044B \u043C\u043D\u043E\u0433\u0438\u0445 \u0442\u0438\u043F\u043E\u0432 \u043A\u043B\u0435\u0442\u043E\u043A. \u0421\u043F\u0435\u043A\u0442\u0440\u0438\u043D \u0444\u043E\u0440\u043C\u0438\u0440\u0443\u0435\u0442 \u0434\u043B\u0438\u043D\u043D\u044B\u0435 \u043C\u043E\u043B\u0435\u043A\u0443\u043B\u044B \u0441\u0442\u0440\u0443\u043A\u0442\u0443\u0440\u043D\u043E\u0439 \u0441\u0435\u0442\u043A\u0438 \u0438 \u0438\u0433\u0440\u0430\u0435\u0442 \u0432\u0430\u0436\u043D\u0443\u044E \u0440\u043E\u043B\u044C \u0432 \u043F\u043E\u0434\u0434\u0435\u0440\u0436\u0430\u043D\u0438\u0438 \u0446\u0435\u043B\u043E\u0441\u0442\u043D\u043E\u0441\u0442\u0438 \u043A\u043B\u0435\u0442\u043E\u0447\u043D\u043E\u0439 \u043C\u0435\u043C\u0431\u0440\u0430\u043D\u044B \u0438 \u0441\u0442\u0440\u0443\u043A\u0442\u0443\u0440\u044B \u0446\u0438\u0442\u043E\u0441\u043A\u0435\u043B\u0435\u0442\u0430. \u041A\u0430\u043A \u043F\u043E\u043A\u0430\u0437\u0430\u043B\u0430 \u043A\u0440\u0438\u043E\u044D\u043B\u0435\u043A\u0442\u0440\u043E\u043D\u043D\u0430\u044F \u0442\u043E\u043C\u043E\u0433\u0440\u0430\u0444\u0438\u044F, \u0444\u043E\u0440\u043C\u0438\u0440\u0443\u0435\u043C\u0430\u044F \u0441 \u0443\u0447\u0430\u0441\u0442\u0438\u0435\u043C \u0441\u043F\u0435\u043A\u0442\u0440\u0438\u043D\u0430 \u0441\u0435\u0442\u043A\u0430 \u0438\u043C\u0435\u0435\u0442 \u0433\u0435\u0442\u0435\u0440\u043E\u0433\u0435\u043D\u043D\u0443\u044E \u0441\u0442\u0440\u0443\u043A\u0442\u0443\u0440\u0443, \u043A\u043E\u0442\u043E\u0440\u0430\u044F \u043C\u0435\u043D\u044F\u0435\u0442\u0441\u044F \u043F\u0440\u0438 \u0440\u0430\u0441\u0442\u044F\u0436\u0435\u043D\u0438\u0438 \u043A\u043B\u0435\u0442\u043E\u0447\u043D\u043E\u0439 \u043C\u0435\u043C\u0431\u0440\u0430\u043D\u044B."@ru . . "Spectrin is a cytoskeletal protein that lines the intracellular side of the plasma membrane in eukaryotic cells. Spectrin forms pentagonal or hexagonal arrangements, forming a scaffold and playing an important role in maintenance of plasma membrane integrity and cytoskeletal structure. The hexagonal arrangements are formed by tetramers of spectrin subunits associating with short actin filaments at either end of the tetramer. These short actin filaments act as junctional complexes allowing the formation of the hexagonal mesh. The protein is named spectrin since it was first isolated as a major protein component of human red blood cells which had been treated with mild detergents; the detergents lysed the cells and the hemoglobin and other cytoplasmic components were washed out. In the light microscope the basic shape of the red blood cell could still be seen as the spectrin-containing submembranous cytoskeleton preserved the shape of the cell in outline. This became known as a red blood cell \"ghost\" (spectre), and so the major protein of the ghost was named spectrin. In certain types of brain injury such as diffuse axonal injury, spectrin is irreversibly cleaved by the proteolytic enzyme calpain, destroying the cytoskeleton. Spectrin cleavage causes the membrane to form blebs and ultimately to be degraded, usually leading to the death of the cell. Spectrin subunits may also be cleaved by caspase family enzymes, and calpain and caspase produce different spectrin breakdown products which can be detected by western blotting with appropriate antibodies. Calpain cleavage may indicate activation of necrosis, while caspase cleavage may indicate apoptosis."@en . "La spectrine est un t\u00E9tram\u00E8re constitu\u00E9 de deux sous-unit\u00E9s nomm\u00E9es respectivement \u03B1 et \u03B2, qui fixent les filaments d'actine du cytosquelette \u00E0 la membrane plasmique par des prot\u00E9ines intrins\u00E8ques \u00E0 cette derni\u00E8re. Elle a un r\u00F4le de stabilit\u00E9 m\u00E9canique."@fr . . . . "Espectrina"@ca . . "L'espectrina \u00E9s una prote\u00EFna del citoesquelet que cobreix la part intracel\u00B7lular de la membrana plasm\u00E0tica de molts tipus de c\u00E8l\u00B7lules adoptant disposicions pentagonals o hexagonals, donant suport estructural i jugant un paper important en el manteniment de la integritat de la membrana plasm\u00E0tica i de l'estructura del citoesquelet. Les disposicions hexagonals s\u00F3n formades per tetr\u00E0mers d'espectrina associades a curts filaments d'actina en els extrems del tetr\u00E0mer. Aquests curts filaments d'actina actuen com complexos d'uni\u00F3 permetent la formaci\u00F3 de la xarxa hexagonal. En alguns tipus de lesions cerebrals, com \u00E9s la lesi\u00F3 axonal difosa, l'espectrina \u00E9s irreversiblement trencada per l'enzim proteol\u00EDtic calpina, destruint el citoesquelet. La divisi\u00F3 de l'espectrina causa bombolles i fins i tot la degeneraci\u00F3, que normalment porta a la mort de cel\u00B7lular."@ca . . . . . "\u0421\u043F\u0435\u043A\u0442\u0440\u0438\u043D"@ru . "Espektrinak zelula eukariotikoen mintzaren alde zitoplasmatikoan kokatzen diren proteina periferikozko zuntzak dira eta zitoeskeletoaren osagai kontsideratzen dira. Globulu gorrietan oso ugaria da espektrina, zelula mintzeko proteinen %25a hartzen du. Espektrinen funtzioa zelula mintzaren osotasuna eta zitoeskeletoaren egitura mantentzea da, bi alde ahur dituen itxura berezi hori emanez."@eu . . . "\u8840\u5F71\u86CB\u767D"@zh . . . . "Espektrinak zelula eukariotikoen mintzaren alde zitoplasmatikoan kokatzen diren proteina periferikozko zuntzak dira eta zitoeskeletoaren osagai kontsideratzen dira. Globulu gorrietan oso ugaria da espektrina, zelula mintzeko proteinen %25a hartzen du. Espektrinen funtzioa zelula mintzaren osotasuna eta zitoeskeletoaren egitura mantentzea da, bi alde ahur dituen itxura berezi hori emanez."@eu . . "Spektrin"@de . "9705"^^ . . "La spettrina \u00E8 una proteina citoscheletrica presente sul versante interno della membrana citoplasmatica delle cellule eucariotiche. Isolata per la prima volta dagli eritrociti, riveste un ruolo importante nel mantenimento dell'integrit\u00E0 della membrana plasmatica e struttura citoscheletrica. La membrana plasmatica conferisce agli eritrociti la possibilit\u00E0 di modificare velocemente la loro forma per poter scorrere anche nel lume dei pi\u00F9 piccoli capillari che spesso hanno un diametro comparabile con quello dello stesso eritrocita. La composizione della membrana plasmatica \u00E8 simile a quella di tutte le altre cellule, \u00E8 dunque costituita da un doppio strato fosfolipidico inframmezzato da colesterolo, in cui sono immerse proteine estrinseche ed intrinseche, altre invece formano lo scheletro di membrana. Questa sottile maglia \u00E8 formata principalmente da filamenti di spettrina \u03B1 e \u03B2 e da microfilamenti di actina, che si connettono alle proteine del sovrastante doppio strato lipidico, interagendo con esse e determinando la grande deformabilit\u00E0 e flessibilit\u00E0 della membrana dell'eritrocita. Mutazioni che coinvolgono la spettrina comunemente causano difetti ereditari dell'eritrocita, tra cui ellissocitosi ereditaria e sferocitosi ereditaria."@it . "\u0633\u0628\u0643\u062A\u0631\u064A\u0646"@ar . "La spectrine est un t\u00E9tram\u00E8re constitu\u00E9 de deux sous-unit\u00E9s nomm\u00E9es respectivement \u03B1 et \u03B2, qui fixent les filaments d'actine du cytosquelette \u00E0 la membrane plasmique par des prot\u00E9ines intrins\u00E8ques \u00E0 cette derni\u00E8re. Elle a un r\u00F4le de stabilit\u00E9 m\u00E9canique."@fr . . "Spektrin ist ein Proteinkomplex und ein wesentlicher Bestandteil des Zytoskeletts der Erythrozyten, kommt aber auch in anderen Zellen vor. Es stabilisiert zusammen mit Aktin die Innenseite der Zellmembran und somit die gesamte Zelle. Genetische Defekte im SPTA1-Gen verursachen die Erbkrankheiten der heredit\u00E4ren Sph\u00E4rozytose Typ 3, Typ 2 und .Mutationen im SPTB-Gen k\u00F6nnen Sph\u00E4rozytose Typ 1 und Elliptozytose Typ 3 verursachen. Mutationen im Gen SPTBN2, das das Protein betaIII-Spektrin kodiert, verursachen beim Menschen die spinozerebell\u00E4re Ataxie Typ 5 (SCA5). In einem Mausmodell wurde gefunden, dass ohne das full-length betaIII-Spektrin die Symptome der humanen SCA5 reproduziert werden. Dazu geh\u00F6ren Gang-Ataxie, Tremor, Verlust der motorischen Koordination, Verlust von Purkinjezellen und Kleinhirn-Atrophie."@de . . . . "\u30B9\u30DA\u30AF\u30C8\u30EA\u30F3\uFF08Spectrin\uFF09\u306F\u7D30\u80DE\u9AA8\u683C\u306E\u30BF\u30F3\u30D1\u30AF\u8CEA\u3067\u3001\u4E94\u91CF\u4F53\u304B\u516D\u91CF\u4F53\u3092\u4F5C\u3063\u3066\u591A\u304F\u306E\u7A2E\u985E\u306E\u7D30\u80DE\u306E\u7D30\u80DE\u819C\u306E\u5185\u5074\u306B\u4F4D\u7F6E\u3057\u3066\u3044\u308B\u3002\u7D30\u80DE\u306E\u5F62\u3092\u7DAD\u6301\u3059\u308B\u8DB3\u5834\u3068\u3057\u3066\u50CD\u304D\u3001\u7D30\u80DE\u819C\u306E\u69CB\u9020\u3092\u7DAD\u6301\u3059\u308B\u306E\u306B\u91CD\u8981\u306A\u5F79\u5272\u3092\u679C\u305F\u3057\u3066\u3044\u308B\u3002\u516D\u91CF\u4F53\u578B\u306F\u3001\u30B9\u30DA\u30AF\u30C8\u30EA\u30F3\u306E\u56DB\u91CF\u4F53\u306E\u4E21\u7AEF\u306B\u30A2\u30AF\u30C1\u30F3\u306E\u77ED\u9396\u304C\u3064\u3044\u3066\u3044\u308B\u3002\u3053\u306E\u30A2\u30AF\u30C1\u30F3\u7E4A\u7DAD\u306F\u516D\u89D2\u5F62\u306E\u7DB2\u76EE\u306E\u7D50\u5408\u90E8\u3068\u306A\u3063\u3066\u3044\u308B\u3002 \u3073\u307E\u3093\u6027\u8EF8\u7D22\u640D\u50B7\u306A\u3069\u306E\u8133\u306E\u5916\u50B7\u3092\u53D7\u3051\u308B\u3068\u3001\u30B9\u30DA\u30AF\u30C8\u30EA\u30F3\u306F\u30AB\u30EB\u30D1\u30A4\u30F3\u306B\u3088\u308B\u4E0D\u53EF\u9006\u7684\u306A\u5207\u65AD\u3092\u53D7\u3051\u3001\u7D30\u80DE\u9AA8\u683C\u304C\u7834\u58CA\u3055\u308C\u308B\u3002\u30B9\u30DA\u30AF\u30C8\u30EA\u30F3\u306E\u5207\u65AD\u306F\u3001\u7D30\u80DE\u819C\u306B\u6F3F\u6DB2\u306B\u3088\u308B\u6C34\u75B1\u3092\u751F\u3058\u3055\u305B\u3001\u7D30\u80DE\u3092\u6B7B\u306B\u81F3\u3089\u3057\u3081\u308B\u3002"@ja . . "1106992491"^^ . "Spektrin ist ein Proteinkomplex und ein wesentlicher Bestandteil des Zytoskeletts der Erythrozyten, kommt aber auch in anderen Zellen vor. Es stabilisiert zusammen mit Aktin die Innenseite der Zellmembran und somit die gesamte Zelle. Genetische Defekte im SPTA1-Gen verursachen die Erbkrankheiten der heredit\u00E4ren Sph\u00E4rozytose Typ 3, Typ 2 und .Mutationen im SPTB-Gen k\u00F6nnen Sph\u00E4rozytose Typ 1 und Elliptozytose Typ 3 verursachen."@de . . "Spectrine"@fr . 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